Basal mitophagy is widespread in Drosophila but minimally affected by loss of Pink1 or parkin JJ Lee, A Sanchez-Martinez, AM Zarate, C Benincá, U Mayor, MJ Clague, ... Journal of Cell Biology 217 (5), 1613-1622, 2018 | 285 | 2018 |
Gαq signalling: the new and the old G Sanchez-Fernandez, S Cabezudo, C Garcia-Hoz, C Beninca, ... Cellular signalling 26 (5), 833-848, 2014 | 126 | 2014 |
Neural stem cells traffic functional mitochondria via extracellular vesicles L Peruzzotti-Jametti, JD Bernstock, CM Willis, G Manferrari, R Rogall, ... PLoS biology 19 (4), e3001166, 2021 | 122 | 2021 |
Rapamycin rescues mitochondrial myopathy via coordinated activation of autophagy and lysosomal biogenesis G Civiletto, SA Dogan, R Cerutti, G Fagiolari, M Moggio, C Lamperti, ... EMBO molecular medicine 10 (11), e8799, 2018 | 104 | 2018 |
Perturbed redox signaling exacerbates a mitochondrial myopathy SA Dogan, R Cerutti, C Beninca, G Brea-Calvo, HT Jacobs, M Zeviani, ... Cell Metabolism 28 (5), 764-775. e5, 2018 | 90 | 2018 |
Ablation of the stress protease OMA1 protects against heart failure in mice R Acin-Perez, AV Lechuga-Vieco, M del Mar Munoz, R Nieto-Arellano, ... Science translational medicine 10 (434), eaan4935, 2018 | 80 | 2018 |
Inhibition of proteasome rescues a pathogenic variant of respiratory chain assembly factor COA7 K Mohanraj, M Wasilewski, C Benincá, D Cysewski, J Poznanski, ... EMBO molecular medicine 11 (5), e9561, 2019 | 64 | 2019 |
Chronic genetic damages in Geophagus brasiliensis exposed to anthropic impact in Estuarine Lakes at Santa Catarina Coast–Southern of Brazil C Benincá, W Ramsdorf, T Vicari, CA de Oliveira Ribeiro, MI de Almeida, ... Environmental monitoring and assessment 184, 2045-2056, 2012 | 47 | 2012 |
Selective disruption of mitochondrial thiol redox state in cells and in vivo LM Booty, JM Gawel, F Cvetko, ST Caldwell, AR Hall, JF Mulvey, ... Cell chemical biology 26 (3), 449-461. e8, 2019 | 44 | 2019 |
A new non-canonical pathway of Gαq protein regulating mitochondrial dynamics and bioenergetics C Benincá, J Planagumà, A de Freitas Shuck, R Acín-Perez, JP Muñoz, ... Cellular signalling 26 (5), 1135-1146, 2014 | 41 | 2014 |
Mutation in the MICOS subunit gene APOO (MIC26) associated with an X-linked recessive mitochondrial myopathy, lactic acidosis, cognitive impairment and autistic features C Benincá, V Zanette, M Brischigliaro, M Johnson, A Reyes, DA do Valle, ... Journal of medical genetics 58 (3), 155-167, 2021 | 40 | 2021 |
Inhibition of ATP synthase reverse activity restores energy homeostasis in mitochondrial pathologies R Acin‐Perez, C Benincá, L Fernandez del Rio, C Shu, S Baghdasarian, ... The EMBO journal 42 (10), e111699, 2023 | 25 | 2023 |
Expanding the molecular and phenotypic spectrum of truncating MT-ATP6 mutations E Bugiardini, E Bottani, S Marchet, OV Poole, C Beninca, A Horga, ... Neurology: Genetics 6 (1), e381, 2020 | 23 | 2020 |
Utilization of human samples for assessment of mitochondrial bioenergetics: Gold standards, limitations, and future perspectives R Acin-Perez, C Benincá, B Shabane, OS Shirihai, L Stiles Life 11 (9), 949, 2021 | 22 | 2021 |
APOPT 1/COA 8 assists COX assembly and is oppositely regulated by UPS and ROS A Signes, R Cerutti, AS Dickson, C Benincá, EC Hinchy, D Ghezzi, ... EMBO molecular medicine 11 (1), e9582, 2019 | 21 | 2019 |
Opa1 overexpression protects from early-onset Mpv17−/−-related mouse kidney disease M Luna-Sanchez, C Benincá, R Cerutti, G Brea-Calvo, A Yeates, ... Molecular Therapy 28 (8), 1918-1930, 2020 | 10 | 2020 |
NDUFV1 mutations in complex I deficiency: Case reports and review of symptoms V Zanette, D Valle, BA Telles, AJ Robinson, V Monteiro, MLSF Santos, ... Genetics and Molecular Biology 44, e20210149, 2021 | 8 | 2021 |
Neurodevelopmental regression, severe generalized dystonia, and metabolic acidosis caused by POLR3A mutations V Zanette, A Reyes, M Johnson, D do Valle, AJ Robinson, V Monteiro, ... Neurology: Genetics 6 (6), e521, 2020 | 5 | 2020 |
Neural stem cells traffic functional mitochondria via extracellular vesicles to correct mitochondrial dysfunction in target cells L Peruzzotti-Jametti, JD Bernstock, G Manferrari, R Rogall, ... bioRxiv, 2020.01. 29.923441, 2020 | 5 | 2020 |
A mammalian-specific Alex3/Gαq protein complex regulates mitochondrial trafficking, dendritic complexity, and neuronal survival I Izquierdo-Villalba, S Mirra, Y Manso, A Parcerisas, J Rubio, J Del Valle, ... Science Signaling 17 (822), eabq1007, 2024 | 1 | 2024 |