| Modulation of mtDNA copy number ameliorates the pathological consequences of a heteroplasmic mtDNA mutation in the mouse R Filograna, C Koolmeister, M Upadhyay, A Pajak, P Clemente, R Wibom, ... Science Advances 5 (4), eaav9824, 2019 | 128 | 2019 |
| Cox25 teams up with Mss51, Ssc1, and Cox14 to regulate mitochondrial cytochrome c oxidase subunit 1 expression and assembly in Saccharomyces cerevisiae F Fontanesi, P Clemente, A Barrientos Journal of Biological Chemistry 286 (1), 555-566, 2011 | 95 | 2011 |
| Defects of mitochondrial RNA turnover lead to the accumulation of double-stranded RNA in vivo A Pajak, I Laine, P Clemente, N El-Fissi, FA Schober, C Maffezzini, ... PLoS Genetics 15 (7), e1008240, 2019 | 61 | 2019 |
| Mitochondrial polyadenylation is a one-step process required for mRNA integrity and tRNA maturation A Bratic, P Clemente, J Calvo-Garrido, C Maffezzini, A Felser, R Wibom, ... PLoS genetics 12 (5), e1006028, 2016 | 59 | 2016 |
| hCOA3 stabilizes cytochrome c oxidase 1 (COX1) and promotes cytochrome c oxidase assembly in human mitochondria P Clemente, S Peralta, A Cruz-Bermudez, L Echevarría, F Fontanesi, ... Journal of Biological Chemistry 288 (12), 8321-8331, 2013 | 56 | 2013 |
| SQSTM1/p62-directed metabolic reprogramming is essential for normal neurodifferentiation J Calvo-Garrido, C Maffezzini, FA Schober, P Clemente, E Uhlin, M Kele, ... Stem cell reports 12 (4), 696-711, 2019 | 49 | 2019 |
| Modeling human mitochondrial diseases in flies Á Sánchez-Martínez, N Luo, P Clemente, C Adán, R Hernández-Sierra, ... Biochimica et Biophysica Acta (BBA)-Bioenergetics 1757 (9-10), 1190-1198, 2006 | 41 | 2006 |
| Glutamyl-tRNAGln amidotransferase is essential for mammalian mitochondrial translation in vivo L Echevarria, P Clemente, R Hernandez-Sierra, ME Gallardo, ... Biochemical Journal 460 (1), 91-101, 2014 | 37 | 2014 |
| The one-carbon pool controls mitochondrial energy metabolism via complex I and iron-sulfur clusters FA Rosenberger, D Moore, I Atanassov, MF Moedas, P Clemente, ... Science Advances 7 (8), eabf0717, 2021 | 35 | 2021 |
| SUV3 helicase is required for correct processing of mitochondrial transcripts P Clemente, A Pajak, I Laine, R Wibom, A Wedell, C Freyer, ... Nucleic acids research 43 (15), 7398-7413, 2015 | 30 | 2015 |
| Coiled coil domain-containing protein 56 (CCDC56) is a novel mitochondrial protein essential for cytochrome c oxidase function S Peralta, P Clemente, Á Sánchez-Martínez, M Calleja, ... Journal of Biological Chemistry 287 (29), 24174-24185, 2012 | 28 | 2012 |
| Mutations in the mitochondrial tryptophanyl‐tRNA synthetase cause growth retardation and progressive leukoencephalopathy C Maffezzini, I Laine, C Dallabona, P Clemente, J Calvo‐Garrido, ... Molecular genetics & genomic medicine 7 (6), e654, 2019 | 20 | 2019 |
| Evaluation of mitochondrial function and metabolic reprogramming during tumor progression in a cell model of skin carcinogenesis CG Vallejo, A Cruz-Bermúdez, P Clemente, R Hernández-Sierra, ... Biochimie 95 (6), 1171-1176, 2013 | 19 | 2013 |
| Myoglobinopathy is an adult-onset autosomal dominant myopathy with characteristic sarcoplasmic inclusions M Olivé, M Engvall, G Ravenscroft, M Cabrera-Serrano, H Jiao, ... Nature communications 10 (1), 1396, 2019 | 18 | 2019 |
| A multi-systemic mitochondrial disorder due to a dominant p. Y955H disease variant in DNA polymerase gamma T Siibak, P Clemente, A Bratic, H Bruhn, TES Kauppila, B Macao, ... Human molecular genetics 26 (13), 2515-2525, 2017 | 18 | 2017 |
| ANGEL2 phosphatase activity is required for non-canonical mitochondrial RNA processing P Clemente, J Calvo-Garrido, SF Pearce, FA Schober, M Shigematsu, ... Nature Communications 13 (1), 5750, 2022 | 6 | 2022 |
| Human COA3 is an oligomeric highly flexible protein in solution JL Neira, S Martínez-Rodríguez, JG Hernandez-Cifre, A Camara-Artigas, ... Biochemistry 55 (45), 6209-6220, 2016 | 3 | 2016 |
| Modulation of mtDNA copy number ameliorates the pathological consequences of a heteroplasmic mtDNA mutation in the mouse. Sci Adv. 2019; 5 (4): eaav9824 R Filograna, C Koolmeister, M Upadhyay, A Pajak, P Clemente, R Wibom | 3 | |
| Dysfunction of Drosophila mitochondrial carrier homolog (Mtch) alters apoptosis and disturbs development C González, L Martínez‐Sánchez, P Clemente, JM Toivonen, ... FEBS Open Bio, 2023 | 2 | 2023 |
| Intergenomic nuclear-mitochondrial cross-talk in Drosophila melanogaster L Echevarría, Á Sánchez-Martínez, P Clemente, R Hernández-Sierra, ... Landes Bioscience, 2010 | 2 | 2010 |
