Loss of C9 ORF 72 impairs autophagy and synergizes with polyQ Ataxin‐2 to induce motor neuron dysfunction and cell death C Sellier, ML Campanari, C Julie Corbier, A Gaucherot, I Kolb‐Cheynel, ... The EMBO journal 35 (12), 1276-1297, 2016 | 437 | 2016 |
Loss of function of C9orf72 causes motor deficits in a zebrafish model of amyotrophic lateral sclerosis S Ciura, S Lattante, I Le Ber, M Latouche, H Tostivint, A Brice, E Kabashi Annals of neurology 74 (2), 180-187, 2013 | 429 | 2013 |
Loss of VPS13C function in autosomal-recessive parkinsonism causes mitochondrial dysfunction and increases PINK1/Parkin-dependent mitophagy S Lesage, V Drouet, E Majounie, V Deramecourt, M Jacoupy, A Nicolas, ... The American Journal of Human Genetics 98 (3), 500-513, 2016 | 416 | 2016 |
Transient receptor potential vanilloid 1 is required for intrinsic osmoreception in organum vasculosum lamina terminalis neurons and for normal thirst responses to systemic … S Ciura, CW Bourque Journal of Neuroscience 26 (35), 9069-9075, 2006 | 327 | 2006 |
Oxytocin-induced analgesia and scratching are mediated by the vasopressin-1A receptor in the mouse A Schorscher-Petcu, S Sotocinal, S Ciura, A Dupré, J Ritchie, RE Sorge, ... Journal of Neuroscience 30 (24), 8274-8284, 2010 | 204 | 2010 |
Overexpression of the serine elastase inhibitor elafin protects transgenic mice from hypoxic pulmonary hypertension SHE Zaidi, XM You, S Ciura, M Husain, M Rabinovitch Circulation 105 (4), 516-521, 2002 | 189 | 2002 |
Defining the genetic connection linking amyotrophic lateral sclerosis (ALS) with frontotemporal dementia (FTD) S Lattante, S Ciura, GA Rouleau, E Kabashi Trends in Genetics 31 (5), 263-273, 2015 | 153 | 2015 |
Hypertonicity sensing in organum vasculosum lamina terminalis neurons: a mechanical process involving TRPV1 but not TRPV4 S Ciura, W Liedtke, CW Bourque Journal of Neuroscience 31 (41), 14669-14676, 2011 | 144 | 2011 |
Methylene Blue Protects against TDP-43 and FUS Neuronal Toxicity in C. elegans and D. rerio A Vaccaro, SA Patten, S Ciura, C Maios, M Therrien, P Drapeau, ... Public Library of Science 7 (7), e42117, 2012 | 115 | 2012 |
TRPV1 gene required for thermosensory transduction and anticipatory secretion from vasopressin neurons during hyperthermia R Sharif-Naeini, S Ciura, CW Bourque Neuron 58 (2), 179-185, 2008 | 100 | 2008 |
Neuroleptics as therapeutic compounds stabilizing neuromuscular transmission in amyotrophic lateral sclerosis SA Patten, D Aggad, J Martinez, E Tremblay, J Petrillo, GAB Armstrong, ... JCI insight 2 (22), 2017 | 97 | 2017 |
Contribution of TRPV channels to osmosensory transduction, thirst, and vasopressin release R Sharif-Naeini, S Ciura, Z Zhang, CW Bourque Kidney international 73 (7), 811-815, 2008 | 93 | 2008 |
Sqstm1 knock-down causes a locomotor phenotype ameliorated by rapamycin in a zebrafish model of ALS/FTLD S Lattante, H de Calbiac, I Le Ber, A Brice, S Ciura, E Kabashi Human molecular genetics 24 (6), 1682-1690, 2015 | 88 | 2015 |
ΔN-TRPV1: a molecular co-detector of body temperature and osmotic stress C Zaelzer, P Hua, M Prager-Khoutorsky, S Ciura, DL Voisin, W Liedtke, ... Cell reports 13 (1), 23-30, 2015 | 84 | 2015 |
Suppressed smooth muscle proliferation and inflammatory cell invasion after arterial injury in elafin-overexpressing mice SHE Zaidi, XM You, S Ciura, S O’Blenes, M Husain, M Rabinovitch The Journal of clinical investigation 105 (12), 1687-1695, 2000 | 84 | 2000 |
Neurophysiological characterization of mammalian osmosensitive neurones CW Bourque, S Ciura, E Trudel, TJE Stachniak, R Sharif‐Naeini Experimental physiology 92 (3), 499-505, 2007 | 77 | 2007 |
Neuromuscular junction impairment in amyotrophic lateral sclerosis: reassessing the role of acetylcholinesterase ML Campanari, MS García-Ayllón, S Ciura, J Sáez-Valero, E Kabashi Frontiers in molecular neuroscience 9, 160, 2016 | 75 | 2016 |
Hes6 inhibits astrocyte differentiation and promotes neurogenesis through different mechanisms S Jhas, S Ciura, S Belanger-Jasmin, Z Dong, E Llamosas, FM Theriault, ... Journal of Neuroscience 26 (43), 11061-11071, 2006 | 74 | 2006 |
Osmotic and thermal control of magnocellular neurosecretory neurons – role of an N‐terminal variant of trpv1 JR Sudbury, S Ciura, R Sharif‐Naeini, CW Bourque European Journal of Neuroscience 32 (12), 2022-2030, 2010 | 70 | 2010 |
The most prevalent genetic cause of ALS-FTD, C9orf72 synergizes the toxicity of ATXN2 intermediate polyglutamine repeats through the autophagy pathway S Ciura, C Sellier, ML Campanari, N Charlet-Berguerand, E Kabashi Autophagy 12 (8), 1406-1408, 2016 | 59 | 2016 |