Mutant huntingtin's interaction with mitochondrial protein Drp1 impairs mitochondrial biogenesis and causes defective axonal transport and synaptic degeneration in Huntington's … UP Shirendeb, MJ Calkins, M Manczak, V Anekonda, B Dufour, ... Human molecular genetics 21 (2), 406-420, 2012 | 377 | 2012 |
Preclinical safety of RNAi-mediated HTT suppression in the rhesus macaque as a potential therapy for Huntington's disease JL McBride, MR Pitzer, RL Boudreau, B Dufour, T Hobbs, SR Ojeda, ... Molecular Therapy 19 (12), 2152-2162, 2011 | 308 | 2011 |
Home improvement: C57BL/6J mice given more naturalistic nesting materials build better nests SE Hess, S Rohr, BD Dufour, BN Gaskill, EA Pajor, JP Garner Journal of the American Association for Laboratory Animal Science 47 (6), 25-31, 2008 | 239 | 2008 |
Barbering (fur and whisker trimming) by laboratory mice as a model of human trichotillomania and obsessive-compulsive spectrum disorders JP Garner, SM Weisker, B Dufour, JA Mench Comparative medicine 54 (2), 216-224, 2004 | 190 | 2004 |
Social and husbandry factors affecting the prevalence and severity of barbering (‘whisker trimming’) by laboratory mice JP Garner, B Dufour, LE Gregg, SM Weisker, JA Mench Applied Animal Behaviour Science 89 (3-4), 263-282, 2004 | 133 | 2004 |
AAV-PHP. B administration results in a differential pattern of CNS biodistribution in non-human primates compared with mice WA Liguore, JS Domire, D Button, Y Wang, BD Dufour, S Srinivasan, ... Molecular Therapy 27 (11), 2018-2037, 2019 | 123 | 2019 |
Fragile X syndrome and associated disorders: Clinical aspects and pathology MJ Salcedo-Arellano, B Dufour, Y McLennan, V Martinez-Cerdeno, ... Neurobiology of disease 136, 104740, 2020 | 113 | 2020 |
Intrajugular vein delivery of AAV9-RNAi prevents neuropathological changes and weight loss in Huntington's disease mice BD Dufour, CA Smith, RL Clark, TR Walker, JL McBride Molecular Therapy 22 (4), 797-810, 2014 | 90 | 2014 |
Experimental models of anxiety for drug discovery and brain research PC Hart, CL Bergner, AN Smolinsky, BD Dufour, RJ Egan, JL LaPorte, ... Mouse models for drug discovery: methods and protocols, 299-321, 2010 | 80 | 2010 |
Reverse-translational biomarker validation of Abnormal Repetitive Behaviors in mice: an illustration of the 4P's modeling approach JP Garner, CM Thogerson, BD Dufour, H Würbel, JD Murray, JA Mench Behavioural brain research 219 (2), 189-196, 2011 | 74 | 2011 |
Nutritional up-regulation of serotonin paradoxically induces compulsive behavior. BD Dufour, O Adeola, HW Cheng, SS Donkin, JD Klein, EA Pajor, ... Nutritional neuroscience 13 (6), 256-264, 2010 | 47 | 2010 |
Single nucleotide seed modification restores in vivo tolerability of a toxic artificial miRNA sequence in the mouse brain AM Monteys, RM Spengler, BD Dufour, MS Wilson, CK Oakley, ... Nucleic acids research 42 (21), 13315-13327, 2014 | 43 | 2014 |
Neuronal and glial cell number is altered in a cortical layer-specific manner in autism C Falcone, NY Mevises, T Hong, B Dufour, X Chen, SC Noctor, ... Autism 25 (8), 2238-2253, 2021 | 37 | 2021 |
Drinking alcohol has sex-dependent effects on pair bond formation in prairie voles AMJ Anacker, TH Ahern, CM Hostetler, BD Dufour, ML Smith, DL Cocking, ... Proceedings of the National Academy of Sciences 111 (16), 6052-6057, 2014 | 30 | 2014 |
Analysis of abnormal repetitive behaviors in experimental animal models PC Hart, CL Bergner, BD Dufour, AN Smolinsky, RJ Egan, JL LaPorte, ... Translational neuroscience and its advancement of animal research ethics …, 2009 | 25 | 2009 |
Corticosterone dysregulation exacerbates disease progression in the R6/2 transgenic mouse model of Huntington's disease BD Dufour, JL McBride Experimental neurology 283, 308-317, 2016 | 24 | 2016 |
An ethological analysis of barbering behavior. BD Dufour, JP Garner Cambridge University Press, 2010 | 20 | 2010 |
Insight and Recommendations for Fragile X-Premutation-Associated Conditions from the Fifth International Conference on FMR1 Premutation F Tassone, D Protic, EG Allen, AD Archibald, A Baud, TW Brown, ... Cells 12 (18), 2330, 2023 | 19 | 2023 |
GABAARα2 is decreased in the axon initial segment of pyramidal cells in specific areas of the prefrontal cortex in autism T Hong, C Falcone, B Dufour, S Amina, RP Castro, J Regalado, ... Neuroscience 437, 76-86, 2020 | 16 | 2020 |
Decreased number and increased activation state of astrocytes in gray and white matter of the prefrontal cortex in autism G Vakilzadeh, C Falcone, B Dufour, T Hong, SC Noctor, ... Cerebral Cortex 32 (21), 4902-4912, 2022 | 14 | 2022 |