| Revertants, low temperature, and correctors reveal the mechanism of F508del-CFTR rescue by VX-809 and suggest multiple agents for full correction CM Farinha, J King-Underwood, M Sousa, AR Correia, BJ Henriques, ... Chemistry & biology 20 (7), 943-955, 2013 | 194 | 2013 |
| Emerging roles for riboflavin in functional rescue of mitochondrial β-oxidation flavoenzymes B J Henriques, R K Olsen, P Bross, C M Gomes Current medicinal chemistry 17 (32), 3842-3854, 2010 | 108 | 2010 |
| Role of Flavinylation in a Mild Variant of Multiple Acyl-CoA Dehydrogenation Deficiency A molecular rationale for the effects of riboflavin supplementation BJ Henriques, JV Rodrigues, RK Olsen, P Bross, CM Gomes Journal of Biological Chemistry 284 (7), 4222-4229, 2009 | 96 | 2009 |
| Electron transfer flavoprotein and its role in mitochondrial energy metabolism in health and disease BJ Henriques, RKJ Olsen, CM Gomes, P Bross Gene 776, 145407, 2021 | 73 | 2021 |
| Cofactors and metabolites as potential stabilizers of mitochondrial acyl-CoA dehydrogenases TG Lucas, BJ Henriques, JV Rodrigues, P Bross, N Gregersen, ... Biochimica et Biophysica Acta (BBA)-Molecular Basis of Disease 1812 (12 …, 2011 | 53 | 2011 |
| Cofactors and metabolites as protein folding helpers in metabolic diseases J V Rodrigues, B J Henriques, T G Lucas, C M Gomes Current topics in medicinal chemistry 12 (22), 2546-2559, 2012 | 38 | 2012 |
| Therapeutic approaches using riboflavin in mitochondrial energy metabolism disorders B J Henriques, T G Lucas, C M Gomes Current drug targets 17 (13), 1527-1534, 2016 | 28 | 2016 |
| Mutational hotspots in electron transfer flavoprotein underlie defective folding and function in multiple acyl-CoA dehydrogenase deficiency BJ Henriques, P Bross, CM Gomes Biochimica et Biophysica Acta (BBA)-Molecular Basis of Disease 1802 (11 …, 2010 | 26 | 2010 |
| Ethylmalonic encephalopathy ETHE1 R163W/R163Q mutations alter protein stability and redox properties of the iron centre BJ Henriques, TG Lucas, JV Rodrigues, JH Frederiksen, MS Teixeira, ... PLoS One 9 (9), e107157, 2014 | 23 | 2014 |
| A polymorphic position in electron transfer flavoprotein modulates kinetic stability as evidenced by thermal stress BJ Henriques, MT Fisher, P Bross, CM Gomes FEBS letters 585 (3), 505-510, 2011 | 20 | 2011 |
| Biophysical and Spectroscopic Methods for Monitoring Protein Misfolding and Amyloid Aggregation JS Cristóvão, BJ Henriques, CM Gomes Protein Misfolding Diseases, 3-18, 2019 | 18 | 2019 |
| Mutations at the flavin binding site of ETF: QO yield a MADD-like severe phenotype in Drosophila E Alves, BJ Henriques, JV Rodrigues, P Prudêncio, H Rocha, L Vilarinho, ... Biochimica et Biophysica Acta (BBA)-Molecular Basis of Disease 1822 (8 …, 2012 | 15 | 2012 |
| Probing the mechanism of rubredoxin thermal unfolding in the absence of salt bridges by temperature jump experiments BJ Henriques, LM Saraiva, CM Gomes Biochemical and biophysical research communications 333 (3), 839-844, 2005 | 14 | 2005 |
| Potential complementation effects of two disease-associated mutations in tetrameric glutaryl-CoA dehydrogenase is due to inter subunit stability-activity counterbalance JV Ribeiro, TG Lucas, P Bross, CM Gomes, BJ Henriques Biochimica et Biophysica Acta (BBA)-Proteins and Proteomics 1868 (1), 140269, 2020 | 12 | 2020 |
| Conformational analysis of the riboflavin-responsive ETF: QO-p. Pro456Leu variant associated with mild multiple acyl-CoA dehydrogenase deficiency TG Lucas, BJ Henriques, CM Gomes Biochimica et Biophysica Acta (BBA)-Proteins and Proteomics 1868 (6), 140393, 2020 | 11 | 2020 |
| Molecular and Clinical Investigations on Portuguese Patients with Multiple acyl-CoA Dehydrogenase Deficiency BJ Henriques, TG Lucas, E Martins, A Gaspar, A Bandeira, C Nogueira, ... Current molecular medicine 19 (7), 487-493, 2019 | 11 | 2019 |
| Combined spectroscopic and calorimetric characterisation of rubredoxin reversible thermal transition BJ Henriques, LM Saraiva, CM Gomes JBIC Journal of Biological Inorganic Chemistry 11 (1), 73-81, 2006 | 10 | 2006 |
| Deglutarylation of glutaryl-CoA dehydrogenase by deacylating enzyme SIRT5 promotes lysine oxidation in mice DP Bhatt, CA Mills, KA Anderson, BJ Henriques, TG Lucas, S Francisco, ... Journal of Biological Chemistry 298 (4), 2022 | 7 | 2022 |
| Thermal Shift and Stability Assays of Disease-Related Misfolded Proteins Using Differential Scanning Fluorimetry TG Lucas, CM Gomes, BJ Henriques Protein Misfolding Diseases, 255-264, 2019 | 7 | 2019 |
| Riboflavin (vitamin B2) and mitochondrial energy BJ Henriques, CM Gomes Molecular Nutrition, 225-244, 2020 | 5 | 2020 |
