WFH guidelines for the management of hemophilia A Srivastava, E Santagostino, A Dougall, S Kitchen, M Sutherland, ... Haemophilia 26, 1-158, 2020 | 1405 | 2020 |
Antioxidants reduce endoplasmic reticulum stress and improve protein secretion JD Malhotra, H Miao, K Zhang, A Wolfson, S Pennathur, SW Pipe, ... Proceedings of the National Academy of Sciences 105 (47), 18525-18530, 2008 | 780 | 2008 |
Efficacy, safety, and pharmacokinetics of emicizumab prophylaxis given every 4 weeks in people with haemophilia A (HAVEN 4): a multicentre, open-label, non-randomised phase 3 study SW Pipe, M Shima, M Lehle, A Shapiro, S Chebon, K Fukutake, NS Key, ... The Lancet Haematology 6 (6), e295-e305, 2019 | 357 | 2019 |
Bleeding due to disruption of a cargo-specific ER-to-Golgi transport complex B Zhang, MA Cunningham, WC Nichols, JA Bernat, U Seligsohn, SW Pipe, ... Nature genetics 34 (2), 220-225, 2003 | 323 | 2003 |
International workshop on immune tolerance induction: consensus recommendations1 DM DIMICHELE, WK Hoots, SW Pipe, GE Rivard, E Santagostino Haemophilia 13, 1-22, 2007 | 312 | 2007 |
Bioengineering of coagulation factor VIII for improved secretion HZ Miao, N Sirachainan, L Palmer, P Kucab, MA Cunningham, ... Blood 103 (9), 3412-3419, 2004 | 293 | 2004 |
Valoctocogene roxaparvovec gene therapy for hemophilia A MC Ozelo, J Mahlangu, KJ Pasi, A Giermasz, AD Leavitt, M Laffan, ... New England Journal of Medicine 386 (11), 1013-1025, 2022 | 249 | 2022 |
Life in the shadow of a dominant partner: the FVIII-VWF association and its clinical implications for hemophilia A SW Pipe, RR Montgomery, KP Pratt, PJ Lenting, D Lillicrap Blood, The Journal of the American Society of Hematology 128 (16), 2007-2016, 2016 | 213 | 2016 |
Long-term outcomes with emicizumab prophylaxis for hemophilia A with or without FVIII inhibitors from the HAVEN 1-4 studies MU Callaghan, C Negrier, I Paz-Priel, T Chang, S Chebon, M Lehle, ... Blood, The Journal of the American Society of Hematology 137 (16), 2231-2242, 2021 | 211 | 2021 |
Differential interaction of coagulation factor VIII and factor V with protein chaperones calnexin and calreticulin SW Pipe, JA Morris, J Shah, RJ Kaufman Journal of Biological Chemistry 273 (14), 8537-8544, 1998 | 207 | 1998 |
New therapies for hemophilia AC Weyand, SW Pipe Blood, The Journal of the American Society of Hematology 133 (5), 389-398, 2019 | 172 | 2019 |
Mannose-dependent endoplasmic reticulum (ER)-Golgi intermediate compartment-53-mediated ER to Golgi trafficking of coagulation factors V and VIII M Moussalli, SW Pipe, HP Hauri, WC Nichols, D Ginsburg, RJ Kaufman Journal of Biological Chemistry 274 (46), 32539-32542, 1999 | 165 | 1999 |
Functional roles of the factor VIII B domain SW Pipe Haemophilia 15 (6), 1187-1196, 2009 | 151 | 2009 |
Mutagenesis of a potential immunoglobulin-binding protein-binding site enhances secretion of coagulation factor VIII M Swaroop, M Moussalli, SW Pipe, RJ Kaufman Journal of Biological Chemistry 272 (39), 24121-24124, 1997 | 149 | 1997 |
Characterization of a genetically engineered inactivation-resistant coagulation factor VIIIa SW Pipe, RJ Kaufman Proceedings of the National Academy of Sciences 94 (22), 11851-11856, 1997 | 147 | 1997 |
Four hydrophobic amino acids of the factor VIII C2 domain are constituents of both the membrane-binding and von Willebrand factor-binding motifs GE Gilbert, RJ Kaufman, AA Arena, H Miao, SW Pipe Journal of Biological Chemistry 277 (8), 6374-6381, 2002 | 144 | 2002 |
Recombinant clotting factors SW Pipe Thrombosis and haemostasis 99 (11), 840-850, 2008 | 143 | 2008 |
Gene therapy with etranacogene dezaparvovec for hemophilia B SW Pipe, FWG Leebeek, M Recht, NS Key, G Castaman, W Miesbach, ... New England Journal of Medicine 388 (8), 706-718, 2023 | 138 | 2023 |
Mild hemophilia A caused by increased rate of factor VIII A2 subunit dissociation: evidence for nonproteolytic inactivation of factor VIIIa in vivo SW Pipe, AN Eickhorst, SH McKinley, EL Saenko, RJ Kaufman Blood, The Journal of the American Society of Hematology 93 (1), 176-183, 1999 | 136 | 1999 |
Biosynthesis, assembly and secretion of coagulation factor VIII. RJ Kaufman, SW Pipe, L Tagliavacca, M Swaroop, M Moussalli Blood coagulation & fibrinolysis: an international journal in haemostasis …, 1997 | 130 | 1997 |