organelles by the autophagic-lysosomal pathway is essential for tissue homeostasis.
Defects of this degradative system have a role in various diseases, but little is known about
autophagy in muscular dystrophies. We have previously found that muscular dystrophies
linked to collagen VI deficiency show dysfunctional mitochondria and spontaneous
apoptosis, leading to myofiber degeneration. Here we demonstrate that this persistence of …