Peutz–Jeghers syndrome is a rare autosomal dominantly inherited condition, characterized
by the presence of hamartomatous gastrointestinal polyps and mucocutaneous
pigmentation. Patients with this syndrome can be associated with other neoplasms such as
ovarian neoplasms known as sex-cord tumor with annular tubules that are associated in one
third of the cases with this syndrome and other types of malignancies. We report a 42-year-
old woman with a history of Peutz–Jeghers Syndrome and bilateral breast cancer that …