Vascular Ehlers-Danlos syndrome: literature review and surgical management of intracranial vascular complications
F Olubajo, C Kaliaperumal, KA Choudhari - Clinical Neurology and …, 2020 - Elsevier
Abstract Vascular Ehlers-Danlos (vEDS) is a rare form of the Ehlers-Danlos Syndrome
(EDS) where arterial fragility results from mutations in the gene that encodes type III
collagen. The disease can lead to major neurological complications including carotico-
cavernous fistulae (CCF), aneurysms of the Circle of Willis and endovascular procedures
have an increased risk profile due to the delicate vasculature. Management of intracranial
disease in vEDS requires an intricate understanding of the syndrome but is still associated …
(EDS) where arterial fragility results from mutations in the gene that encodes type III
collagen. The disease can lead to major neurological complications including carotico-
cavernous fistulae (CCF), aneurysms of the Circle of Willis and endovascular procedures
have an increased risk profile due to the delicate vasculature. Management of intracranial
disease in vEDS requires an intricate understanding of the syndrome but is still associated …
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