Epidemiological changes in Eisenmenger syndrome in the Nordic region in 1977–2012

CS Hjortshøj, AS Jensen, K Sørensen, E Nagy… - Heart, 2017 - heart.bmj.com
Objective Improved diagnostic tools, timely closure of the shunt and a better understanding
of the complexity of Eisenmenger syndrome (ES) have led to improved care and treatment in …

Past and current cause-specific mortality in Eisenmenger syndrome

CMS Hjortshøj, A Kempny, AS Jensen… - European Heart …, 2017 - academic.oup.com
Aims Eisenmenger syndrome (ES) is associated with considerable morbidity and mortality.
Therapeutic strategies have changed during the 2000s in conjunction with an emphasis on …

Survival prospects of treatment naïve patients with Eisenmenger: a systematic review of the literature and report of own experience

GP Diller, A Kempny, R Inuzuka, R Radke, SJ Wort… - Heart, 2014 - heart.bmj.com
Objectives To investigate survival in patients with Eisenmenger syndrome based on a
systematic review of the literature and reanalysis of data. We specifically tested the …

Declining incidence and prevalence of Eisenmenger syndrome in the developed world: a triumph of modern medicine

A Kempny, K Dimopoulos, MA Gatzoulis - Heart, 2017 - heart.bmj.com
In 1897, Dr Victor Eisenmenger described a 32-year-old man with a history of cyanosis and
progressive exertional breathlessness since childhood. The patient developed heart failure …

Presentation, survival prospects, and predictors of death in Eisenmenger syndrome: a combined retrospective and case–control study

GP Diller, K Dimopoulos, CS Broberg… - European heart …, 2006 - academic.oup.com
Abstract Aims To characterize contemporary Eisenmenger patients at a large centre for adult
congenital heart disease, assess survival prospects, and identify predictors of death in this …

Predictors of death in contemporary adult patients with Eisenmenger syndrome: a multicenter study

A Kempny, CS Hjortshøj, H Gu, W Li, AR Opotowsky… - Circulation, 2017 - Am Heart Assoc
Background: Eisenmenger syndrome is associated with substantial morbidity and mortality.
There is no consensus, however, on mortality risk stratification. We aimed to investigate …

The Belgian Eisenmenger syndrome registry: implications for treatment strategies?

A Van de Bruaene, M Delcroix, A Pasquet… - Acta …, 2009 - Taylor & Francis
Objective—Pulmonary arterial hypertension (PAH), associated with congenital heart disease
(CHD), usually results from a systemic-to-pulmonary shunt. Eisenmenger syndrome (ES) is …

Current therapy and outcome of Eisenmenger syndrome: data of the German National Register for congenital heart defects

GP Diller, MA Körten, UMM Bauer, O Miera… - European Heart …, 2016 - academic.oup.com
Aims We aimed to assess the contemporary outcome of Eisenmenger syndrome (ES),
delineate the use of disease targeting therapies (DTT) in these patients and to investigate …

Determinants of sudden cardiac death in adult patients with Eisenmenger syndrome

A Chiriac, DC Riley, M Russell, JP Moore… - Journal of the …, 2020 - Am Heart Assoc
Background Patients with Eisenmenger syndrome are known to have a high incidence of
sudden cardiac death (SCD), yet the underlying causes are not well understood. We sought …

Poor prognosis and related factors in adults with Eisenmenger syndrome

H Oya, N Nagaya, M Uematsu, T Satoh… - American heart …, 2002 - Elsevier
Background Little information is available regarding the clinical history and long-term
prognosis of patients with Eisenmenger syndrome without diagnosis until adulthood. The …