Background Studies have described illness associated with cystic fibrosis (CF) early in life,
but there is no comprehensive accounting of the prevalence and ages of disease …

As a testimony to advances in patient care, more individuals with cystic fibrosis are surviving
into their adult years than ever before. The clinical epidemiology of this complex multi-organ …

The past decade has seen significant advances in understanding of the pathogenesis and
progression of lung disease in cystic fibrosis (CF). Pulmonary inflammation, infection, and …

Once considered a pediatric disease with a poor prognosis, individuals born with cystic
fibrosis (CF) today can expect to live well into adulthood. The implementation of …

Cystic fibrosis (CF) is an autosomal recessive disease characterized by pancreatic
insufficiency and chronic endobronchial airway infection. This latter feature results in …

Cystic fibrosis (CF) lung disease starts early in life and progresses even in the absence of
clinical symptoms. Therefore, sensitive outcome measures to quantify and track these early …

Cystic fibrosis (CF) has been shown to affect people all over the world. While life expectancy
for people with CF has increased substantially, CF is still associated with death in infants …

Considerable advances in cystic fibrosis (CF) research have translated into improved patient
care, reflected by a continuing trend of improving life expectancy in CF patients. This review …

Cystic fibrosis (CF), earlier believed to be non existent in non Caucasians, is now a pan
ethnic disease, having being reported from various regions of the world over last one …

Background Newborn screening allows novel treatments for cystic fibrosis (CF) to be trialled
in early childhood before irreversible lung injury occurs. As respiratory exacerbations are a …