Focal changes in the globi pallidi associated with neurological dysfunction in methylmalonic acidaemia

C De Sousa, AT Piesowicz, EM Brett… - …, 1989 - thieme-connect.com
Neurological abnormalities are common in patients with organic acidaemias and sometimes
these are distinctive. Lesions in various parts of the brain are increasingly being recognised …

Acute pediatric hyperammonemia: current diagnosis and management strategies

N Savy, D Brossier, C Brunel-Guitton… - Hepatic medicine …, 2018 - Taylor & Francis
Acute hyperammonemia may induce a neurologic impairment leading to an acute life-
threatening condition. Coma duration, ammonia peak level, and hyperammonemia duration …