Many lung diseases result in fibrotic remodelling. Fibrotic lung disorders can be divided into
diseases with known and unknown aetiology. Among those with unknown aetiology …

Idiopathic pulmonary fibrosis (IPF) is a unique type of chronic fibrosing lung disease of
unknown etiology. The sequence of the pathogenic mechanisms is unknown, but the …

Idiopathic pulmonary fibrosis (IPF) is characterized by the progressive and ultimately fatal
accumulation of fibroblasts and extracellular matrix in the lung that distorts its architecture …

Abstract Background and Aim Idiopathic pulmonary fibrosis (IPF) is characterized by
hyperplasia of type II alveolar epithelial cells, aggregation of activated (myo) fibroblasts and …

Idiopathic pulmonary fibrosis (IPF) is the most frequent fibrotic diffuse parenchymal lung
disease. Its prognosis is devastating:> 50% of the patients die within 3 years after diagnosis …

Idiopathic pulmonary fibrosis (IPF), a progressive and relentless lung scarring of unknown
etiology, has been recognized as the most lethal interstitial lung disease. Despite the …

Idiopathic pulmonary fibrosis (IPF) is a devastating disease characterized by severe and
progressive scar formation in the gas-exchange regions of the lung. Despite years of …

Idiopathic pulmonary fibrosis (IPF) is a life-threatening condition, with a median survival of<
3 yrs. The pathophysiology is not fully understood, but chronic injury of alveolar epithelial …

Idiopathic pulmonary fibrosis (IPF) is a progressive and irreversible fibrosing interstitial
pneumonia of unknown aetiology that usually leads to respiratory failure and death within 5 …

Idiopathic pulmonary fibrosis is a progressive lung disease that carries a poor prognosis and
for which there are no effective therapies. Although the excessive deposition of extracellular …