The Belgian Eisenmenger syndrome registry: implications for treatment strategies?

A Van de Bruaene, M Delcroix, A Pasquet… - Acta …, 2009 - Taylor & Francis
Objective—Pulmonary arterial hypertension (PAH), associated with congenital heart disease
(CHD), usually results from a systemic-to-pulmonary shunt. Eisenmenger syndrome (ES) is …

Eisenmenger syndrome and other types of pulmonary arterial hypertension related to adult congenital heart disease

C Favoccia, AH Constantine, SJ Wort… - Expert review of …, 2019 - Taylor & Francis
Introduction: Eisenmenger syndrome (ES) is the most advanced form of pulmonary arterial
hypertension (PAH) in patients with congenital heart disease (CHD). It is characterised by a …

Eisenmenger syndrome: current perspectives

H Nashat, A Kempny, C McCabe, LC Price… - Research Reports in …, 2017 - Taylor & Francis
Eisenmenger syndrome (ES) is the most severe form of pulmonary arterial hypertension
(PAH) related to congenital heart disease (CHD). It results from a cardiac defect allowing …

Management of pulmonary arterial hypertension associated with congenital systemic-to-pulmonary shunts and Eisenmenger's syndrome

N Galie, A Manes, M Palazzini, L Negro, A Marinelli… - Drugs, 2008 - Springer
A large proportion of patients with congenital heart disease (CHD), in particular those with
relevant systemic-to-pulmonary shunts, will develop pulmonary arterial hypertension (PAH) …

Declining incidence and prevalence of Eisenmenger syndrome in the developed world: a triumph of modern medicine

A Kempny, K Dimopoulos, MA Gatzoulis - Heart, 2017 - heart.bmj.com
In 1897, Dr Victor Eisenmenger described a 32-year-old man with a history of cyanosis and
progressive exertional breathlessness since childhood. The patient developed heart failure …

Eisenmenger syndrome: diagnosis, prognosis and clinical management

A Arvanitaki, G Giannakoulas, H Baumgartner… - Heart, 2020 - heart.bmj.com
Eisenmenger syndrome (ES) represents the most severe phenotype of pulmonary arterial
hypertension (PAH) associated with congenital heart disease (CHD) and occurs in patients …

Past and current cause-specific mortality in Eisenmenger syndrome

CMS Hjortshøj, A Kempny, AS Jensen… - European Heart …, 2017 - academic.oup.com
Aims Eisenmenger syndrome (ES) is associated with considerable morbidity and mortality.
Therapeutic strategies have changed during the 2000s in conjunction with an emphasis on …

[HTML][HTML] Life span of patients with Eisenmenger syndrome is not superior to that of patients with other causes of pulmonary hypertension

B Bonello, S Renard, J Mancini, S Hubert… - Cardiovascular …, 2014 - ncbi.nlm.nih.gov
Background Patients with Eisenmenger syndrome (ES) carry a better prognosis from
diagnosis than patients with other causes of pulmonary hypertension (PH), but their life span …

Pulmonary hypertension in congenital shunts

M Beghetti, C Tissot - Revista Española de Cardiología (English Edition), 2010 - Elsevier
Pulmonary arterial hypertension frequently arises in patients with congenital heart disease.
The vast majority present with congenital cardiac shunts. Initially these may manifest as left …

Pulmonary vasodilator therapy is associated with greater survival in Eisenmenger syndrome

C Arnott, G Strange, A Bullock, AC Kirby, C O'Donnell… - Heart, 2018 - heart.bmj.com
Objective Eisenmenger syndrome (ES) is a severe form of pulmonary hypertension in adults
with congenital heart disease (CHD) and has a poor prognosis. We aimed to understand …