Management of pulmonary arterial hypertension associated with congenital systemic-to-pulmonary shunts and Eisenmenger's syndrome

N Galie, A Manes, M Palazzini, L Negro, A Marinelli… - Drugs, 2008 - Springer
A large proportion of patients with congenital heart disease (CHD), in particular those with
relevant systemic-to-pulmonary shunts, will develop pulmonary arterial hypertension (PAH) …

Pulmonary vascular disease in adults with congenital heart disease

GP Diller, MA Gatzoulis - Circulation, 2007 - Am Heart Assoc
Pulmonary arterial hypertension of variable degree is commonly associated with adult
congenital heart disease. Depending on size and location of the underlying cardiac defect …

Current era survival of patients with pulmonary arterial hypertension associated with congenital heart disease: a comparison between clinical subgroups

A Manes, M Palazzini, E Leci… - European heart …, 2014 - academic.oup.com
Aims This study compared the clinical, functional, and haemodynamic characteristics and
current era survival of subgroups of patients with pulmonary arterial hypertension associated …

Pulmonary arterial hypertension associated with congenital heart disease

M D'Alto, VS Mahadevan - European Respiratory Review, 2012 - Eur Respiratory Soc
Pulmonary arterial hypertension (PAH) is a common complication of congenital heart
disease (CHD), with most cases occurring in patients with congenital cardiac shunts. In …

Pulmonary arterial hypertension in congenital heart disease

JT Granton, M Rabinovitch - Cardiology clinics, 2002 - cardiology.theclinics.com
Pulmonary Arterial Hypertension (PAH) is a recognized complication of congenital cardiac
defects that are characterized by chronic left-to-right shunting. Viktor Eisenmenger initially …

Pulmonary arterial hypertension in adult congenital heart disease

M Brida, MA Gatzoulis - Heart, 2018 - heart.bmj.com
Pulmonary arterial hypertension (PAH) is commonly associated with congenital heart
disease (CHD) and relates to type of the underlying cardiac defects and repair history. Large …

Pulmonary hypertension in adults with congenital heart disease and Eisenmenger syndrome: current advanced management strategies

M D'Alto, GP Diller - Heart, 2014 - heart.bmj.com
The presence of pulmonary arterial hypertension (PAH) increases morbidity and reduces
survival in patients with congenital heart disease (CHD). PAH-CHD is a heterogeneous …

Pulmonary hypertension in children with congenital heart disease (PAH-CHD, PPHVD-CHD). Expert consensus statement on the diagnosis and treatment of …

R Kozlik-Feldmann, G Hansmann, D Bonnet… - Heart, 2016 - heart.bmj.com
Pulmonary arterial hypertension associated with congenital heart disease (PAH-CHD) is a
complex disease that presents with a broad spectrum of morphological and haemodynamic …

Eisenmenger syndrome: a clinical perspective in a new therapeutic era of pulmonary arterial hypertension

M Beghetti, N Galiè - Journal of the American College of Cardiology, 2009 - jacc.org
Eisenmenger syndrome (ES), the most advanced form of pulmonary arterial hypertension
(PAH) associated with congenital heart disease, is a devastating condition that has a …

Pulmonary hypertension associated with congenital heart disease: pulmonary vascular disease: the global perspective

I Adatia, SS Kothari, JA Feinstein - Chest, 2010 - Elsevier
The incidence of congenital heart disease is approximately 8/1,000 live births and appears
to be constant around the world. The currently accepted paradigm for the development of …