Arrhythmogenic cardiomyopathy (ACM) is a genetic heart muscle disease characterised by
substitution of the ventricular myocardium by fibrofatty tissue. 1 The disease was originally
termed 'arrhythmogenic right ventricular (dysplasia/) cardiomyopathy'(ARVC) to define a
condition which distinctively affected the right ventricle (RV) and predisposed to potentially
fatal ventricular arrhythmias, particularly in young individuals and athletes. 2–4 New insights
arising from postmortem investigations, genotype–phenotype correlation studies and …

Arrhythmogenic cardiomyopathy (ACM) is a myocardium disease characterized by
phenotypic features of myocardial scarring due to fibrofatty myocardial replacement often
associated with global or regional ventricular dysfunction. For years after arrhythmogenic
right ventricular cardiomyopathy (ARVC) was first described, the left ventricle (LV) was
generally considered normal or minimally involved. In recent years, however, LV
involvement has been recognized. It usually presents with early-on arrhythmias more than …