Abstract Febrile ulceronecrotic Mucha–Habermann disease (FUMHD) is a rare severe
variant of pityriasis lichenoides et varioliformis acuta characterized clinically by aggressive
ulceronecrotic skin lesions associated with high fever and histologically by features typical of
pityriasis lichenoides et varioliformis acuta. Despite the continuous addition of new case
reports, no definite diagnostic criteria have been established, and an optimum treatment is
still waiting. Herein, we review the different aspects of this rare entity, including …

The Mucha-Habermann disease is an inflammatory disease of the skin and is a variant of
pityriasis lichenoides et varioliformis acuta. We describe the case of a 64-years-old woman
who was admitted for erysipelas of the face. Despite treatment, evolution was marked by the
appearance of a necrotising ulcerative area in the centre of the erysipelas associated with
local oedema and headache. A skin biopsy revealed a pityriasis lichenoides et varioliformis
acuta. Corticosteroids led to a rapid stabilisation of lesions, and after 6 months the patient …