Klippel–Trenaunay syndrome patients often suffer degenerative joint disease at an early
age. Performing arthroplasty in these patients is particularly difficult for a number of reasons.
In this case report, we describe the second reported case of total hip replacement in Klippel–
Trenaunay syndrome, using novel techniques to surmount the problems faced in this
challenging condition.

ABSTRACT Introduction: Klippel-Tranaunay syndrome is a rare congenital condition
characterized by skin angiomas with arteriovenous malformations and hypertrophy of the
soft and bone tissues of one extremity. The clinical case presented herein involved total hip
replacement due to arthrosis secondary to avascular necrosis of the femoral head, which
resulted in the hypervascularity that occurs with this syndrome. A 37 year-old female was
diagnosed with grade IV hip arthrosis and Klippel-Trenaunay syndrome. Laboratory and …