Patients with pulmonary arterial hypertension associated with congenital heart disease
(PAH–CHD), particularly those with Eisenmenger syndrome (ES), are significantly impaired …

Background: Pulmonary arterial hypertension (PAH) associated with congenital heart
disease (APAH-CHD) is a subgroup of PAH including four different forms sharing similar …

Congenital heart disease (CHD), the most common inborn defect, affects approximately 1%
of all newborns worldwide. Advances in its diagnosis and treatment have led to a dramatic …

Background The purpose of this registry was to provide insights into the characteristics,
treatments and survival of patients with PAH-CHD in China. Methods Patients diagnosed …

The number of patients with pulmonary arterial hypertension related to congenital heart
disease (PAH‐CHD) seen in specialist centers continues to increase. The extreme end of …

Aims This study compared the clinical, functional, and haemodynamic characteristics and
current era survival of subgroups of patients with pulmonary arterial hypertension associated …

Uncorrected congenital heart disease (CHD) frequently leads to pulmonary arterial
hypertension (PAH), the most severe form of which is Eisenmenger syndrome (ES). We …

The population growth of adults with congenital heart disease (ACHD) continues to
accelerate, unveiling a group of patients with unique and complex medical problems. On its …

Pulmonary arterial hypertension (PAH) in congenital heart disease (PAH–CHD) is the result
of numerous pathomechanistic pathways affecting the pulmonary vascular bed and leading …

Abstract Background Patients with CHD-PAH have a limited prognosis. In daily practice,
combination therapy is often initiated after a clinical event. Although clinical events have …