Classification criteria for autoinflammatory recurrent fevers

M Gattorno, M Hofer, S Federici, F Vanoni… - Annals of the …, 2019 - ard.bmj.com
Background Different diagnostic and classification criteria are available for hereditary
recurrent fevers (HRF)—familial Mediterranean fever (FMF), tumour necrosis factor receptor …

IgA vasculitis

E Pillebout, C Sunderkötter - Seminars in immunopathology, 2021 - Springer
IgA vasculitis (IgAV) is an inflammation of small vessels caused by perivascular deposition
of IgA and activation of neutrophils. It may present as systemic vasculitis (IgAV-Henoch …

European consensus-based recommendations for diagnosis and treatment of immunoglobulin A vasculitis—the SHARE initiative

S Ozen, SD Marks, P Brogan, N Groot… - …, 2019 - academic.oup.com
Abstract Objectives IgA vasculitis (IgAV, formerly known as Henoch–Schönlein purpura) is
the most common cause of systemic vasculitis in childhood. To date, there are no …

[HTML][HTML] IgA vasculitis update: epidemiology, pathogenesis, and biomarkers

L Xu, Y Li, X Wu - Frontiers in Immunology, 2022 - frontiersin.org
Immunoglobulin A vasculitis (IgAV), formerly known as Henoch-Schönlein purpura, is the
most common systemic vasculitis in children, characterized by diverse clinical …

Mutant adenosine deaminase 2 in a polyarteritis nodosa vasculopathy

P Navon Elkan, SB Pierce, R Segel… - … England Journal of …, 2014 - Mass Medical Soc
Background Polyarteritis nodosa is a systemic necrotizing vasculitis with a pathogenesis that
is poorly understood. We identified six families with multiple cases of systemic and …

[PDF][PDF] Henoch-Schönlein purpura: a literature review

LE Hetland, KS Susrud… - Acta dermato …, 2017 - medicaljournalssweden.se
Henoch-Sch? nlein purpura is the most common childhood vasculitis, but may also affect
adults. This article reviews the literature since 2011 on advances in diagnosis, clinical …

[HTML][HTML] Childhood IgA vasculitis (Henoch Schonlein purpura)—advances and knowledge gaps

L Oni, S Sampath - Frontiers in pediatrics, 2019 - frontiersin.org
Immunoglobulin A vasculitis (IgAV; formerly Henoch Schonlein Purpura) is the most
common form of childhood vasculitis. It can occur in any age and peaks around 4–6 years …

ADA2 deficiency (DADA2) as an unrecognised cause of early onset polyarteritis nodosa and stroke: a multicentre national study

R Caorsi, F Penco, A Grossi, A Insalaco… - Annals of the …, 2017 - ard.bmj.com
Objectives To analyse the prevalence of CECR1 mutations in patients diagnosed with early
onset livedo reticularis and/or haemorrhagic/ischaemic strokes in the context of inflammation …

Henoch–Schönlein purpura nephritis in children

JC Davin, R Coppo - Nature Reviews Nephrology, 2014 - nature.com
Henoch–Schönlein purpura (HSP) is the most common vasculitis in children, in whom
prognosis is mostly dependent upon the severity of renal involvement. Nephritis is observed …

Epidemiology of Takayasu arteritis

F Onen, N Akkoc - La Presse Médicale, 2017 - Elsevier
Takayasu arteritis (TA), a granulomatous large vessel vasculitis involves mostly the aorta
and its proximal branches and occurs most commonly in young females. The data on the …