Pulmonary Langerhans'-cell histiocytosis forms part of a spectrum of diseases characterized
by monoclonal proliferation and infiltration of organs by Langerhans' cells (Table 1). 1 …

Primary vascular neoplasms of the spleen constitute the majority of nonhematolymphoid
splenic tumors. The benign primary vascular tumors include hemangioma, hamartoma, and …

Adult pulmonary Langerhans' cell histiocytosis is a rare disorder of unknown aetiology that
occurs predominantly in young smokers, with an incidence peak at 20–40 yrs of age. In …

The diffuse cystic lung diseases (DCLDs) are a group of pathophysiologically heterogenous
processes that are characterized by the presence of multiple spherical or irregularly shaped …

Interstitial lung diseases (also known as diffuse infiltrative lung diseases) are a
heterogeneous group of parenchymal lung disorders of known or unknown cause. These …

Abstract Pulmonary Langerhans Cell Histiocytosis (PLCH) is a relatively uncommon lung
disease that generally, but not invariably, occurs in cigarette smokers. The pathologic …

Pulmonary Langerhans cell histiocytosis (PLCH) is an isolated form of Langerhans cell
histiocytosis that primarily affects cigarette smokers. PLCH is characterized by …

In the early 1950s Lichtenstein introduced the term histiocytosis X to describe a group of
syndromes with seemingly unrelated clinical features, but whose pathological findings were …

Background The natural history of pulmonary Langerhans cell histiocytosis (PLCH) has
been unclear due to the absence of prospective studies. The rate of patients who experience …

The world of rare interstitial lung diseases (ILDs) is diverse and complex. Diagnosis and
therapy usually pose challenges. This review describes a selection of rare and ultrarare …