Early and late outcomes of cardiovascular surgery in patients with Ehlers-Danlos Syndrome

MF Elsisy, A Pochettino, JA Dearani… - World Journal for …, 2021 - journals.sagepub.com
Background Cardiovascular surgical outcomes reports are few for vascular type IV of Ehlers-
Danlos Syndrome (vEDS) compared to non-vascular types I-III (nEDS). Methods To define …

Utilization of echocardiography in Ehlers‐Danlos syndrome

KK Rauser‐Foltz, LJ Starr… - Congenital heart …, 2019 - Wiley Online Library
Objectives This study assessed the frequency and utility of echocardiographic examination
in patients with all forms of Ehlers‐Danlos syndrome and sought to identify clinical variables …

Pregnancy and fetal outcomes in patients with Ehlers-Danlos syndrome: a nationally representative analysis

N Alrifai, L Alhuneafat, A Jabri, MU Khalid… - Current problems in …, 2023 - Elsevier
Short Abstract Cardiovascular complications occur frequently in Ehlers-Danlos syndrome
(EDS). Pregnancy outcomes, however, are not well established in patients with EDS. We …

Current management of the vascular subtype of Ehlers–Danlos syndrome

E Benrashid, JW Ohman - Current Opinion in Cardiology, 2020 - journals.lww.com
Although new consensus guidelines have emerged to facilitate the diagnosis of those with
vEDS, there remain limitations in terms of interventions and medical therapy that can be …

Cardiovascular Complications In Hospitalized Patients With Ehlers Danlos Syndrome (EDS) A Retrospective Cohort Study

MH Al-Taei, A Alshami - Journal of Cardiac Failure, 2024 - Elsevier
Introduction Ehlers Danlos syndromes (EDS) constitute a group of connective tissue
diseases characterized by collagen synthesis abnormalities. The manifestation of EDS …

Increased need for gastrointestinal surgery and increased risk of surgery-related complications in patients with Ehlers-Danlos syndrome: a systematic review

ML Kulas Søborg, J Leganger, J Rosenberg… - Digestive …, 2017 - karger.com
Abstract Background/Aims: Ehlers-Danlos syndromes (EDSs) constitute a rare group of
inherited connective tissue diseases, characterized by multisystemic manifestations and …

[HTML][HTML] Molecular diagnosis in vascular Ehlers-Danlos syndrome predicts pattern of arterial involvement and outcomes

S Shalhub, JH Black III, AC Cecchi, Z Xu… - Journal of vascular …, 2014 - Elsevier
Objective The management of arterial pathology in individuals with vascular Ehlers-Danlos
syndrome (vEDS) remains a challenge. Here we describe the correlation between COL3A1 …

[HTML][HTML] Cardiac involvement in classical or hypermobile Ehlers–Danlos syndrome is uncommon

SL Paige, KM Lechich, ESS Tierney, RT Collins II - Genetics in Medicine, 2020 - Elsevier
Purpose Cardiac–valvular and vascular Ehlers–Danlos syndrome (EDS) have significant
cardiovascular issues. The prevalence and significance of such abnormalities in classical …

Clinical features of Ehlers-Danlos syndrome

JL Yen, SP Lin, MR Chen, DM Niu - Journal of the Formosan Medical …, 2006 - Elsevier
BACKGROUND/PURPOSE: Ehlers-Danlos syndrome (EDS) is a clinically and genetically
heterogeneous connective tissue disorder characterized by hyperextensibility of the skin …

[HTML][HTML] A multi-institutional experience in vascular Ehlers-Danlos syndrome diagnosis

S Shalhub, PH Byers, KL Hicks, DM Coleman… - Journal of vascular …, 2020 - Elsevier
Abstract Objective Vascular Ehlers-Danlos syndrome (vEDS) is a rare disorder and 1 of 13
types of EDS. The syndrome results in aortic and arterial aneurysms and dissections at a …