The Nosology of Creutzfeldt‐Jakob Disease and Conditions Related to the Accumulation of PrPCJD in the Nervous System

EP Richardson Jr, CL Masters - Brain Pathology, 1995 - Wiley Online Library
Although typical cases of Creutzfeldt‐Jakob disease are readily recognized pathologically
and clinically, variant forms often pose a diagnostic challenge. From the 1920's, when this …

Homonymous field defect as the first manifestation of Creutzfeldt-Jakob disease

ME Vargas, MJ Kupersmith, PJ Savino, F Petito… - American journal of …, 1995 - Elsevier
Purpose Although in the early stage of Creutzfeldt-Jakob disease most patients have
obvious dementia, we found that the disease can be diagnosed in patients solely on the …

Reversible periodic alternating gaze deviation in hepatic encephalopathy

L Averbuch-Heller, Z Meiner - Neurology, 1995 - AAN Enterprises
Article abstract-We report two patients with hepatic encephalopathy who developed periodic
alternating gaze deviation (PAGD). Neither patient had an evident structural lesion, and the …

Centripetal nystagmus in a case of Creutzfeldt-Jacob disease

C Helmchen, U Büttner - Neuro-ophthalmology, 1995 - Taylor & Francis
Acquired forms of gaze-holding nystagmus usually produce centrifugal nystagmus. The
authors report about a 63-year-old-patient with a rapidly deteriorating syndrome of …

Rapid progressive form of posterior cerebral dysfunction with apperceptive agnosia in a 34-year-old man-another case of heidenhain's syndrome?

J Pantel, RD Bleser, M Schwarz, C Weiller - Neurocase, 1995 - Taylor & Francis
Posterior cortical atrophy (PCA) or progressive posterior cerebral dysfunction is a
neurodegenerative disorder initially dominated by disturbances in higher visual functions …

Familial congenital periodic alternating nystagmus with presumably X-linked dominant inheritance

PLM Huygen, WIM Verhagen, JRM Cruysberg… - Neuro …, 1995 - Taylor & Francis
Familial congenital periodic alternating nystagmus (PAN) with presumably X-linked
dominant inheritance (XLPAN) was observed in the proband and her mother. Many relatives …