Pulmonary arterial hypertension of variable degree is commonly associated with adult
congenital heart disease. Depending on size and location of the underlying cardiac defect …

Eisenmenger syndrome (ES), the most advanced form of pulmonary arterial hypertension
(PAH) associated with congenital heart disease, is a devastating condition that has a …

Pulmonary hypertension remained an unexplained intractable disease with poor prognosis.
In the last 2 decades, however, the diagnosis and treatment methods for this disease …

Background—Advanced therapy (AT) for pulmonary arterial hypertension in the context of
congenital heart disease (Eisenmenger syndrome) improves pulmonary hemodynamics …

Diagnosis and Management of Adult Congenital Heart Disease, by Drs. Gatzoulis, Webb,
and Daubeney, is a practical, one-stop resource designed to help you manage the unique …

The success of lung transplantation has improved over time as evidenced by better long-
term survival and functional outcomes. Despite the success of this procedure, there are …

Numerous studies have attempted to identify recipientrelated characteristics that portend
poor clinical outcomes after lung transplantation. As already covered in the previous parts of …

Eisenmenger syndrome is the most severe and extreme phenotype of pulmonary arterial
hypertension associated with congenital heart disease. A large nonrestrictive systemic left-to …

Eisenmenger syndrome is the most severe form of pulmonary arterial hypertension and
arises on the basis of congenital heart disease with a systemic-to-pulmonary shunt. Due to …

Although new advanced therapies hold promise in PAH secondary to CHD, long-term data
are clearly needed. Advanced therapies should be considered when other causes of …