Pleuroparenchymal fibroelastosis (PPFE) is an unusual pulmonary disease with unique
clinical, radiological, and pathological characteristics. Designated a rare idiopathic …

Background Physicians have few opportunities to perform surgical lung biopsy (SLB) to
diagnose idiopathic pleuroparenchymal fibroelastosis (IPPFE). Therefore, diagnostic criteria …

Change in body composition with skeletal muscle wasting, a major component of pulmonary
cachexia, is associated with mortality in chronic obstructive pulmonary disease and cancer …

Pleuroparenchymal fibroelastosis : Current Opinion in Pulmonary Medicine
Pleuroparenchymal fibroelastosis : Current Opinion in Pulmonary Medicine Log in or …

The world of rare interstitial lung diseases (ILDs) is diverse and complex. Diagnosis and
therapy usually pose challenges. This review describes a selection of rare and ultrarare …

Objective. Idiopathic pleuroparenchymal fibroelastosis (IPPFE) is a rare disease
characterized by predominant upper lobe pulmonary fibrosis of unknown etiology. However …

BACKGROUND Pleuroparenchymal fibroelastosis (PPFE) has been described in
hypersensitivity pneumonitis (HP) yet its functional implications are unclear. Combined …

Background Pleuroparenchymal fibroelastosis (PPFE) is a rare subset of idiopathic
interstitial pneumonias. No large-scale clinical studies of PPFE have been published. The …

Background: Weight loss is frequently reported in patients with idiopathic pulmonary fibrosis
(IPF) and may be associated with worse outcomes in these patients. Objective: The aim of …

Background Clinical course of pleuroparenchymal fibroelastosis (PPFE) shows
considerable variation among patients, but there is no established prognostic prediction …