Background and Objectives To facilitate and improve the diagnostic and therapeutic process
by systematically reviewing studies on patients with primary angiitis of the CNS (PACNS) …

The diagnosis of primary central nervous system (CNS) vasculitis is often difficult. There are
neither specific clinical features nor a classical clinical course, and no blood or imaging …

The European Stroke Organisation (ESO) guideline on Primary Angiitis of the Central
Nervous System (PACNS), developed according to ESO standard operating procedures …

With 16.9 million people who suffered a first-ever stroke in 2010 worldwide, stroke is a very
common vascular disease. Epidemiologic studies have played an essential role in …

Inflammatory rheumatic diseases (IRDs), encompassing a broad spectrum of chronic
disorders, typically necessitate prolonged therapeutic intervention. Nevertheless, these …

Abstract Primary CNS Vasculitis (PCNSV) is a rare, diverse, and polymorphic CNS blood
vessel inflammatory condition. Due to its rarity, clinical variability, heterogeneous imaging …

Background Primary angiitis of the CNS (PACNS) is a process causing variously combined
neurological disturbances. Its rarity and kaleidoscopic presentation make it difficult to …

Primary angiitis of the central nervous system (PACNS) is an inflammatory brain disease
targeting the cerebral blood vessels, leading to a wide spectrum of signs and symptoms …

Vasculitis of the central nervous system can be a localized process, such as primary angiitis
of the central nervous system (PACNS), or systemic vasculitis, such as ANCA-associated …

Central nervous system (CNS) vasculitis (CNS) in systemic erythematosus lupus (SLE) is a
rare and challenging diagnosis. We report four cases of CNS vasculitis that occurred 5 to 16 …