Secondary mitochondrial dysfunction across the spectrum of hereditary and acquired muscle disorders
G Mak, M Tarnopolsky, JQ Lu - Mitochondrion, 2024 - Elsevier
Mitochondria form a dynamic network within skeletal muscle. This network is not only
responsible for producing adenine triphosphate through oxidative phosphorylation, but also …
responsible for producing adenine triphosphate through oxidative phosphorylation, but also …
Characterization of Proteome Changes in Aged and Collagen VI-Deficient Human Pericyte Cultures
M Moriggi, E Torretta, M Cescon, L Russo… - International Journal of …, 2024 - mdpi.com
Pericytes are a distinct type of cells interacting with endothelial cells in blood vessels and
contributing to endothelial barrier integrity. Furthermore, pericytes show mesenchymal stem …
contributing to endothelial barrier integrity. Furthermore, pericytes show mesenchymal stem …
Salbutamol repurposing ameliorates neuromuscular junction defects and muscle atrophy in Col6a1−/− mouse model of collagen VI‐related myopathies
S Calabrò, L Nogara, Y Jian, M Valentin… - Clinical and …, 2024 - pmc.ncbi.nlm.nih.gov
Dear Editor, Collagen VI (ColVI)-related myopathies are a distinct group of progressive
muscle disorders, which include Ullrich congenital muscular dystrophy (UCMD) and …
muscle disorders, which include Ullrich congenital muscular dystrophy (UCMD) and …