[HTML][HTML] Standards for the care of people with cystic fibrosis; establishing and maintaining health

KW Southern, C Addy, SC Bell, A Bevan… - Journal of Cystic …, 2024 - Elsevier
This is the second in a series of four papers updating the European Cystic Fibrosis Society
(ECFS) standards for the care of people with CF. This paper focuses on establishing and …

Dornase alfa in Cystic Fibrosis: Indications, comparative studies and effects on lung clearance index

V Terlizzi, C Castellani, G Taccetti, B Ferrari - Italian Journal of Pediatrics, 2022 - Springer
Cystic fibrosis (CF) is the most common inherited disease in Caucasian populations,
affecting around 50,000 patients in Europe and 30,000 in United States. A mutation in CF …

Effects of CFTR-modulator triple therapy on sinunasal symptoms in children and adults with cystic fibrosis

SFN Bode, H Rapp, N Lienert, H Appel… - European Archives of Oto …, 2023 - Springer
Purpose Sinunasal symptoms and chronic rhinusinutitis are common in patients with cystic
fibrosis. Cystic fibrosis transmembrane regulator (CFTR) modulators have led to dramatic …

Pediatric chronic rhinosinusitis

HH Ramadan - European Archives of Oto-Rhino-Laryngology, 2024 - Springer
Purpose An up-to-date overview of diagnosis, differential diagnosis, comorbidities, and
current medical and surgical management of pediatric chronic rhinosinusitis (PCRS) …

[HTML][HTML] A Decade of Pathogenesis Advances in Non-Type 2 Inflammatory Endotypes in Chronic Rhinosinusitis: 2012–2022

N Cui, X Zhu, C Zhao, C Meng, J Sha… - International archives of …, 2023 - karger.com
Chronic rhinosinusitis (CRS) is a heterogeneous disease characterized by localized
inflammation of the upper airways. CRS includes two main phenotypes, namely, CRS with …

Upper airway disease in adults with cystic fibrosis in the era of CFTR modulators

S Uyttebroek, L Dupont, M Jorissen… - The …, 2023 - Wiley Online Library
Objectives Chronic rhinosinusitis (CRS) is prevalent in people with cystic fibrosis (PwCF)
and is often refractory to treatments. Uncontrolled CRS might negatively impact the lower …

[HTML][HTML] Sinonasal quality of life in primary ciliary dyskinesia

T Stack, M Norris, S Kim, M Lamb… - … forum of allergy & …, 2023 - pmc.ncbi.nlm.nih.gov
Methods: Population and study design This IRB-approved, single-center, retrospective chart
review included CF, PCD, and CRSsNP patients with documented rhinosinusitis disability …

Obstructive sleep apnea and nocturnal hypoxemia in adult patients with cystic fibrosis

M Welsner, S Dietz-Terjung, F Stehling… - BMC Pulmonary …, 2022 - Springer
Background Obstructive sleep apnea (OSA), nocturnal hypoxemia and excessive daytime
sleepiness (EDS) are common comorbidities in people with cystic fibrosis (pwCF). Most of …

Impact of sociodemographic status and sex on chronic rhinosinusitis and olfaction in people with cystic fibrosis

EJ Han, CM Liu, JL Fischer, JC Mace… - … Forum of Allergy & …, 2024 - Wiley Online Library
Background Sociodemographic status (SDS) including race/ethnicity and socioeconomic
status as approximated by education, income, and insurance status impact pulmonary …

Headache and Facial Pain/Pressure in the Chronic Rhinosinusitis Population: A Systematic Review and Meta‐analysis

LD Heiland, HG Farmer, SA Nguyen… - … –Head and Neck …, 2024 - Wiley Online Library
Objective To evaluate the severity and prevalence of headache and facial pain/pressurere in
the chronic rhinosinusitis (CRS) population. Data Sources CINAHL, PubMed, Scopus …