Inner ear malformations are present in 20% of patients with sensorineural hearing loss.
Although the first descriptions date to the 18th century, in recent years the knowledge about …

Inner ear malformations are recognized by imaging in about 20% of children with congenital
sensorineural hearing loss. Normal development of the inner ear structures can be affected …

The use of neonatal hearing screening has enabled the identification of congenital unilateral
sensorineural hearing loss (USNHL) immediately after birth, and today there are several …

Objective To investigate the feasibility of a deep learning method based on a UNETR model
for fully automatic segmentation of the cochlea in temporal bone CT images. Methods The …

Objective A “gold standard” for quantitatively diagnosing inner ear malformations (IEMs) and
a consensus on normative measurements are lacking. Reference ranges and cutoff values …

Objective To examine the effect of vestibular ocular reflex on gross motor development in
children with semicircular canal aplasia and hypoplasia. Study design Case series …

Objective To make evidence-based recommendations for the indications and complications
of Cochlear Implant (CI) surgery in adults and children. Methods Task force members were …

Objectives The aim was to evaluate the cochlear implant (CI) mapping parameters of CI
users with inner ear malformation (IEM) and to reveal the changes in parameters over time …

Despite the low overall prevalence of individual rare diseases, cochlear dysfunction leading
to hearing loss represents a symptom in a large proportion. The aim of this work was to …

OBJECTIVES This paper attempts to create a new classification type of cochlear hypoplasia
(CH)-type malformation taking into consideration of vestibular section and internal auditory …