Hepatic manifestations of cystic fibrosis

S Sakiani, DE Kleiner, T Heller, C Koh - Clinics in liver disease, 2019 - liver.theclinics.com
Cystic fibrosis (CF) is the most common autosomal recessive genetic disorder in white
people, 1, 2 and is also one of the most lethal. 3, 4 It is caused by a mutation in the gene …

Interventions for improving adherence to airway clearance treatment and exercise in people with cystic fibrosis

M Jones, F Moffatt, A Harvey… - Cochrane Database of …, 2023 - cochranelibrary.com
Background Cystic fibrosis (CF) is a life‐limiting genetic disorder predominantly affecting the
lungs and pancreas. Airway clearance techniques (ACTs) and exercise therapy are key …

Cystic fibrosis‐related liver disease is an independent risk factor for mortality and increased health care resource utilization in hospitalized pediatric patients with cystic …

A Thavamani, KK Umapathi, K Kutney… - Pediatric …, 2022 - Wiley Online Library
Background Cystic fibrosis‐related liver disease (CFLD) is more prevalent in recent decades
due to the increasing life expectancy of patients with cystic fibrosis (CF). There is paucity of …

Hospitalization costs of cystic fibrosis in the United States: a retrospective analysis

P Vadagam, KM Kamal - Hospital Practice, 2018 - Taylor & Francis
Objective: To determine patient, hospital, and clinical characteristics associated with the
length of stay (LOS), total hospital charges, and total hospital costs in cystic fibrosis (CF) …

Correlates of distress in young people with cystic fibrosis: the role of self-efficacy and metacognitive beliefs

JK Russell, E Strodl, DJ Kavanagh - Psychology & Health, 2021 - Taylor & Francis
Objectives While significantly elevated distress is repeatedly found amongst young people
with cystic fibrosis, their determinants remain largely unknown. This study explored whether …

[HTML][HTML] Trend analysis of aggregate outcomes in complex health survey data

WM Durand, PC Stey, ES Chen… - AMIA Summits on …, 2018 - ncbi.nlm.nih.gov
Public health and clinical practice pattern trends are often analyzed using complex survey
data. Use of statistical approaches that do not account for survey design predisposes to …

National trends of hospitalizations in cystic fibrosis highlight a need for pediatric to adult transition clinics

ML Ramsey, LF Lara, CE Gariepy, M Abu-El-Haija… - Pancreas, 2021 - journals.lww.com
Objectives We hypothesized that hospitalizations in cystic fibrosis (CF) would reflect the
development of age-related comorbidities. Methods A retrospective analysis was performed …

Analysis of hospital management of chronic respiratory diseases in light of the “Maps of Health Needs” project in Poland

K Jahnz-Różyk… - Advances in …, 2020 - journals.viamedica.pl
Abstract Introduction: The “Maps of Health Needs” project has been carried out in Poland
since 2016 and its purpose is to implement quality-promoting and organisational solutions in …

Have CFTR modulators changed the need for liver and lung transplantation among patients with cystic fibrosis? An analysis of the UNOS database

M Mendizabal, C Cywes, N Muñoz, A Banker… - Liver … - journals.lww.com
Cystic fibrosis (CF) transmembrane conductance regulator (CFTR) modulators were
introduced into the routine care of patients with cystic fibrosis (PwCF) in 2012 (1). The …

Hepatopancreatic syndrome: focus on cystic fibrosis

NB Gubergrits, OV Tsys, NV Byelyayeva - Herald of Pancreatic Club, 2024 - vkp.org.ua
Гепатопанкреатичний синдром: фокус на муковісцидоз Page 1 ВІСНИК КЛУБУ
ПАНКРЕАТОЛОГІВ СЕРПЕНЬ 2024 18 ОГЛЯДИ Удк 616.3600406: 616.37008.6]: 616.2008.6056.7 …