Abstract The 2015 World Health Organization (WHO) Classification of Tumors of the Lung,
Pleura, Thymus and Heart has just been published with numerous important changes from …

Perivascular epithelioid cell tumors, or PEComas, are mesenchymal neoplasms composed
of histologically and immunohistochemically distinctive epithelioid or spindle cells, which are …

Tuberous sclerosis complex is a genetic disorder characterized by hamartomatous lesions
in multiple organs, frequently involving the kidney. We conducted a retrospective review of …

Renal angiomyolipomata. Renal angiomyolipomata can exist as an imaging curiosity or
represent a life-threatening condition. There are likely over 10 million people world-wide …

Pulmonary lymphangioleiomyomatosis (LAM) is a destructive lung disease characterized by
a diffuse hamartomatous proliferation of smooth muscle cells (LAM cells) in the lungs …

Tuberous sclerosis complex (TSC) is an autosomal dominant genetic disease characterized
by hamartomatous tumors involving multiple organs such as the brain, skin, heart, lung and …

The purpose of this article is to review the hereditary renal cystic diseases that can manifest
in children and adults, with specific attention to pathogenesis and imaging features. Various …

Tuberous sclerosis (TSC) is a rare, genetically determined disorder/familial tumor syndrome,
currently diagnosed using specific clinical criteria proposed by Gomez, including the …

Multifocal micronodular pneumocyte hyperplasia is a rare pulmonary manifestation of
tuberous sclerosis complex (TSC) that is a tumor suppressor gene disorder characterized by …

Cystic lung disease is a frequently encountered problem caused by a diverse group of
diseases. Distinguishing true cystic lung disease from other entities, such as cavitary lung …