Pathology of peripheral nerve sheath tumors: diagnostic overview and update on selected diagnostic problems

FJ Rodriguez, AL Folpe, C Giannini, A Perry - Acta neuropathologica, 2012 - Springer
Peripheral nerve sheath tumors are common neoplasms, with classic identifiable features,
but on occasion, they are diagnostically challenging. Although well-defined subtypes of …

Myxofibrosarcoma landscape: Diagnostic pitfalls, clinical management and future perspectives

S Vanni, A De Vita, L Gurrieri, V Fausti… - Therapeutic …, 2022 - journals.sagepub.com
Myxofibrosarcoma (MFS) is a common entity of adult soft tissue sarcomas (STS)
characterized by a predilection of the extremities and a high local recurrence rate. Originally …

Translocation-positive low-grade fibromyxoid sarcoma: clinicopathologic and molecular analysis of a series expanding the morphologic spectrum and suggesting …

L Guillou, J Benhattar, C Gengler… - The American journal …, 2007 - journals.lww.com
Low-grade fibromyxoid sarcomas (LGFMS) bear either the t (7, 16)(q32-34; p11) or t (11,
16)(p11; p11) translocations, resulting in FUS-CREB3L2 or FUS-CREB3L1 fusions …

Fibrosarcoma: a review and update

AL Folpe - Histopathology, 2014 - Wiley Online Library
Adult fibrosarcoma, defined by the W orld H ealth O rganization as a 'malignant neoplasm
composed of fibroblasts with variable collagen production and, in classical cases, a …

Low-grade fibromyxoid sarcoma: clinical, morphologic and genetic features

M Mohamed, C Fisher, K Thway - Annals of diagnostic pathology, 2017 - Elsevier
Low-grade fibromyxoid sarcoma (LGFMS) is a bland spindle cell neoplasm that typically
arises in the deep soft tissues of the proximal extremities or trunk of young adults. The …

EWSR1-CREB3L1 gene fusion: a novel alternative molecular aberration of low-grade fibromyxoid sarcoma

PPL Lau, PCW Lui, GTC Lau, DTW Yau… - The American Journal …, 2013 - journals.lww.com
Low-grade fibromyxoid sarcoma (LGFMS) is an uncommon sarcoma with a deceptively
bland-looking morphology that disguises its malignant clinical behavior. It shows distinctive …

A genetic dichotomy between pure sclerosing epithelioid fibrosarcoma (SEF) and hybrid SEF/low‐grade fibromyxoid sarcoma: a pathologic and molecular study of 18 …

C Prieto‐Granada, L Zhang, HW Chen… - Genes …, 2015 - Wiley Online Library
Sclerosing epithelioid fibrosarcoma (SEF) is a rare soft tissue tumor exhibiting considerable
morphologic overlap with low‐grade fibromyxoid sarcoma (LGFMS). Moreover, both SEF …

In-depth genetic analysis of sclerosing epithelioid fibrosarcoma reveals recurrent genomic alterations and potential treatment targets

E Arbajian, F Puls, CR Antonescu, F Amary… - Clinical Cancer …, 2017 - AACR
Purpose: Sclerosing epithelioid fibrosarcoma (SEF) is a highly aggressive soft tissue
sarcoma closely related to low-grade fibromyxoid sarcoma (LGFMS). Some tumors display …

Predicting master transcription factors from pan-cancer expression data

J Reddy, MAS Fonseca, RI Corona, R Nameki… - Science …, 2021 - science.org
Critical developmental “master transcription factors”(MTFs) can be subverted during
tumorigenesis to control oncogenic transcriptional programs. Current approaches to …

Low‐Grade Fibromyxoid Sarcoma: Incidence, Treatment Strategy of Metastases, and Clinical Significance of the FUS Gene

K Maretty-Nielsen, S Baerentzen, J Keller, HB Dyrop… - Sarcoma, 2013 - Wiley Online Library
Aim. The aim of this study was to assess the incidence of low‐grade fibromyxoid sarcoma
(LGFMS), present treatment results of metastatic LGFMS, and investigate the clinical …