Peripheral muscle dysfunction is an important systemic consequence of cystic fibrosis (CF)
with major clinical implications, such as exercise intolerance and reduced quality of life …

Cardiovascular diseases can be an emerging complication in cystic fibrosis (CF), as the
median life expectancy has improved considerably. The objective of this study was to …

Background Improved exercise capacity (EC) and normal glucose tolerance (NGT) are
independently associated with favorable outcomes in CF, however, little information on this …

Background and objective: Over 2000 genotypes in the cystic fibrosis (CF) gene have been
described. These genotypic differences result in variable clinical manifestations of CF, with …

Background In people with cystic fibrosis (CF), higher exercise capacity is associated with
better health-related quality of life (HRQoL), reduced risk of hospitalisation for a respiratory …

Introduction: Longitudinal data regarding changes in exercise capacity among adult cystic
fibrosis (CF) patients are currently scarce. The aim of this brief report was to assess changes …

Objectives To evaluate feasibility of the Alfred Step Test Exercise Protocol (A‐STEP) for the
assessment of exercise capacity in adults and children with cystic fibrosis (CF); in adults to …

ABSTRACT Background Oxygen uptake (V̇O2) kinetics have been shown to be slowed in
adolescents with cystic fibrosis (CF) during heavy-intensity cycling and maximal exercise …

Cardiac hemodynamic assessment during cardiopulmonary exercise testing (CPET) is
proposed to play an important role in the clinical evaluation of individuals with cystic fibrosis …

Objectives: To evaluate feasibility of the Alfred Step Test Exercise Protocol (A‐STEP) for the
assessment of exercise capacity in adults and children with cystic fibrosis (CF); in adults to …