“Malignant” perivascular epithelioid cell neoplasm: risk stratification and treatment strategies

JS Bleeker, JF Quevedo, AL Folpe - Sarcoma, 2012 - Wiley Online Library
Purpose. Perivascular epithelioid cell tumors (PEComas) are a rare collection of tumors
characterized by a myomelanocytic phenotype, and PEComas occurring in “nonclassic” …

Renal angiomyolipoma without visible fat: Can we make the diagnosis using CT and MRI?

RS Lim, TA Flood, MDF McInnes, LT Lavallee… - European …, 2018 - Springer
Renal angiomyolipomas without visible fat (AML. wovf) are benign masses that are
incidentally discovered mainly in women. AML. wovf are typically homogeneously …

A distinctive subset of PEComas harbors TFE3 gene fusions

P Argani, S Aulmann, PB Illei, GJ Netto… - The American journal …, 2010 - journals.lww.com
Perivascular epithelioid cell neoplasms (PEComas) include the common renal
angiomyolipoma, pulmonary clear cell sugar tumor, lymphangioleiomyomatosis, and less …

Perivascular epithelioid cell tumors (PEComas) harboring TFE3 gene rearrangements lack the TSC2 alterations characteristic of conventional PEComas: further …

I Malinowska, DJ Kwiatkowski, S Weiss… - The American journal …, 2012 - journals.lww.com
tracts. 7–10, 14, 16, 19 The cells comprising these lesions may be variably epithelioid or
spindled in shape and have variable cytoplasm ranging from clear to eosinophilic. By …

Molecular targeted therapy for advanced or metastatic soft tissue sarcoma

J Yuan, X Li, S Yu - Cancer Control, 2021 - journals.sagepub.com
Soft tissue sarcomas are a form of rare and heterogeneous neoplasms with high recurrence
rate and mortality. Over the past decades, less progress has been achieved. Surgical …

Imaging features of primary and metastatic malignant perivascular epithelioid cell tumors

SH Tirumani, AB Shinagare… - American Journal of …, 2014 - Am Roentgen Ray Soc
OBJECTIVE. The objective of our study was to describe the imaging features of primary and
metastatic malignant perivascular epithelioid cell tumors (PEComas). MATERIALS AND …

Cathepsin K expression in a wide spectrum of perivascular epithelioid cell neoplasms (PEC omas): a clinicopathological study emphasizing extrarenal PEC omas

Q Rao, L Cheng, Q Xia, B Liu, L Li, Q Shi, S Shi… - …, 2013 - Wiley Online Library
Aims Recent studies have demonstrated that cathepsin K seems to be a powerful marker in
identifying renal perivascular epithelioid cell neoplasms (PEC omas). However, the …

Management strategies for adults with locally advanced, unresectable or metastatic malignant perivascular epithelioid cell tumor (PEComa): challenges and solutions

AM Czarnecka, J Skoczylas, E Bartnik… - Cancer Management …, 2023 - Taylor & Francis
PEComa (PEC tumor; perivascular epithelioid cell tumors) is a rare group of tumors of
mesenchymal origin composed of perivascular epithelioid cells (PEC) with features of …

Perivascular epithelioid cell tumour: dynamic CT, MRI and clinicopathological characteristics—analysis of 32 cases and review of the literature

Y Tan, H Zhang, EH Xiao - Clinical Radiology, 2013 - Elsevier
AIM: To evaluate the dynamic computed tomography (CT), magnetic resonance imaging
(MRI), and clinicopathological characteristics of perivascular epithelioid cell tumours …

Successful treatment with the mTOR inhibitor everolimus in a patient with perivascular epithelioid cell tumor

C Gennatas, V Michalaki, P Vasilatou Kairi… - World journal of surgical …, 2012 - Springer
Perivascular epithelioid cell tumor (PEComa) is an extremely rare neoplasm that appears to
arise most commonly at visceral (especially gastrointestinal and uterine), retroperitoneal …