Background: This American Thoracic Society, European Respiratory Society, Japanese
Respiratory Society, and Asociación Latinoamericana de Tórax guideline updates prior …

Pulmonary fibrosis is a pathologic process associated with scarring of the lung interstitium.
Interstitial lung diseases (ILDs) encompass a large and heterogenous group of disorders, a …

Abstract Idiopathic Pulmonary Fibrosis (IPF) is a most common progressive interstitial lung
disease (ILD) of unknown etiology, although majority of patients are elderly male smokers …

Rationale: Honeycombing on chest computed tomography (CT) has been described in
diverse forms of interstitial lung disease (ILD); however, its prevalence and association with …

Introduction PROOF (a Prospective Observational Registry to Describe the Disease Course
and Outcomes of Idiopathic Pulmonary Fibrosis) is an ongoing, observational registry …

Background Idiopathic pulmonary fibrosis (IPF) is a progressive disease with a variable
clinical course and high mortality. We used data from a large national US registry of patients …

Purpose Pirfenidone and nintedanib unequivocally inhibit FVC decline, but have been
inconsistently linked to reduced mortality in phase III studies. On the contrary, real-world …

Idiopathic pulmonary fibrosis (IPF) is a chronic, progressive fibrosing interstitial lung disease
of unknown aetiology. Patients typically present with symptoms of chronic dyspnoea and …

While radiography is the first-line imaging technique for evaluation of pulmonary disease,
high-resolution computed tomography (HRCT) provides detailed assessment of the lung …

Background The clinical course and prognosis of progressive fibrosing interstitial lung
diseases (PF-ILDs) vary between individuals. Notably, predictive serum biomarkers for …