Abstract Purpose of Review Chronic thromboembolic pulmonary hypertension (CTEPH),
included in group 4 PH, is an uncommon complication of acute pulmonary embolism (PE), in …

Primary pulmonary artery tumors (PPATs), originating from the pulmonary artery intima, are
rare tumors characterized by pulmonary artery luminal occlusion and pulmonary …

Primary pulmonary artery sarcoma is a rare cardiac tumor with a dismal prognosis without
surgical therapy. It is often confused with the more common chronic pulmonary emboli which …

Introduction Primary pulmonary artery sarcoma (PPAS) is a very rare tumor that mimics
pulmonary embolism (PE) in clinical presentation and on imaging studies, therefore leading …

Background Pulmonary artery intimal sarcoma (PAS) is a very rare disease, its prevalence is
about 0.001–0.003%. PAS is often misdiagnosed as acute or chronic pulmonary …

Objective Primary pulmonary artery sarcoma (PAS) is a rare tumor that originates from the
intimal layer of the pulmonary artery or pulmonary valve and has a poor prognosis. The …

Background Pulmonary artery sarcoma (PAS) is an extremely rare tumour, preferably treated
by surgery. However, the surgical management remains largely debatable, as only less than …

Pulmonary artery stenosis represents a group of disorders involving main, branch or
peripheral pulmonary arteries with pain, dyspnea, hemoptysis or even no symptoms. Early …

Pulmonary artery sarcoma (PAS) is a rare tumour that originates from the intimal layer of the
pulmonary trunk and pulmonary arteries. Diagnosis of PAS is challenging, since it can be …

Background Isolated pulmonary vasculitis (IPV) is a single-organ vasculitis of unknown
etiology and may mimic chronic thromboembolic pulmonary hypertension (CTEPH). The aim …