Mimics of pediatric small vessel primary angiitis of the central nervous system

CM Stredny, MM Blessing, V Yi, ME Ryan… - Annals of …, 2023 - Wiley Online Library
Objective Small vessel primary angiitis of the central nervous system is a rare and often
severe disease characterized by central nervous system‐restricted inflammatory vasculitis …

Current practices in the diagnosis and treatment of Rasmussen syndrome: Results of an international survey

CM Stredny, C Steriade, MT Papadopoulou… - … : European Journal of …, 2024 - Elsevier
Purpose Rasmussen syndrome (RS) is marked by progressive unihemispheric atrophy,
resulting in hemiparesis, refractory epilepsy, and cognitive/language decline. Detailed …

Unilateral Relapsing Primary CNS Vasculitis: Description of 3 Cases From a Single-Institutional Cohort of 216 Cases

C Salvarani, GG Hunder, C Giannini… - Neurology …, 2023 - AAN Enterprises
Objectives To define the frequency and characteristics of patients with unilateral relapsing
involvement in a cohort of patients with adult primary CNS vasculitis (PCNSV). Methods We …

[PDF][PDF] Unilateral primary angiitis of the central nervous system

B Santyr, S Pejhan, Q Zhang, A Budhram - Annals of Neurology, 2021 - researchgate.net
A28-year-old, otherwise healthy female was referred to the neurology clinic after having 3
generalized tonic–clonic seizures over 3 days. Neurologic and general medical …

Focal CNS vasculitis masquerading as new-onset focal aware seizures

D Vibha, R kumar Singh, A Garg… - BMJ Case Reports …, 2023 - casereports.bmj.com
Primary angiitis of the central nervous system (PACNS) is an autoimmune disease with
myriad presentations in the form of headache, focal neurological deficits, seizures and rapid …

Infratentorial MRI findings in Rasmussen encephalitis suggest primary cerebellar involvement

JT Reiter, B David, S Enders, CC Prillwitz… - Neurology …, 2021 - AAN Enterprises
Background and Objective Rasmussen encephalitis (RE) is characterized by its unilateral
cerebral involvement. However, both ipsi-and contralesional cerebellar atrophy have been …

Teaching NeuroImage: Unilateral Primary Angiitis of the CNS

S Alkabie, MT Gray, JC Lau, L Barra, J Mandzia… - Neurology, 2024 - AAN Enterprises
A 48-year-old woman was referred with an 18-year history of focal-onset seizures. She also
reported years-long slowly progressive right-sided weakness that was corroborated on …

A case of childhood unilateral relapsing primary angiitis of the central nervous system

H Onomura, S Furukawa, S Nishida… - …, 2023 - Wiley Online Library
The patient was a 17‐year‐old girl with transient right‐sided weakness and dysesthesia
associated with headache and nausea. Head magnetic resonance imaging (MRI) revealed …

Focal status epilepticus may trigger relapse of primary angiitis of the CNS

A Guilmot, SM Slootjes, T Duprez, J Lelotte… - Epileptic …, 2022 - Wiley Online Library
The role of neuroinflammation in epileptogenesis is extensively investigated, but short‐term
effects of seizures on established CNS pathologies are less studied and less predictable …

AB0790 UNILATERAL RELAPSING PRIMARY CENTRAL NERVOUS SYSTEM VASCULITIS: DESCRIPTION OF 3 CASES FROM A SINGLE INSTITUTIONAL …

C Salvarani, G Hunder, C Giannini, J Huston III… - Annals of the Rheumatic …, 2023 - Elsevier
Background Some cases of unilateral primary central nervous system vasculitis (PCNSV)
with relapsing disease involving the same brain hemisphere have been described [1] …