J Finsterer, C Stöllberger - Cardiology, 2003 - karger.com
Dystrophinopathies are due to mutations in the dystrophin gene on chromosome Xp21. 1 and comprise the allelic entities Duchenne muscular dystrophy (DMD), Becker muscular …
Heart failure is a major cause of death in boys with Duchenne muscular dystrophy. In order to determine if the cardiac function of the mdx mouse is similarly disturbed, we performed …
F Kimura, Y Matsuo, T Nakajima, T Nishikawa… - Radiographics, 2010 - pubs.rsna.org
Myocardial fat is often seen at cardiac computed tomography (CT) and magnetic resonance (MR) imaging of healthy adults and patients with myocardial diseases. Physiologic …
A Florian, A Ludwig, S Rösch, H Yildiz… - European Heart …, 2014 - academic.oup.com
Aim Cardiac involvement with progressive myocardial fibrosis leading to dilated cardiomyopathy is a major cause of death in muscular dystrophy patients. Extracellular …
S Mavrogeni, A Papavasiliou, K Spargias… - BMC neurology, 2010 - Springer
Abstract Background In patients with Duchenne Muscular Dystrophy (DMD), the absent or diminished dystrophin leads to progressive skeletal muscle and heart failure. We evaluated …
G Cannavale, M Francone, N Galea… - BioMed Research …, 2018 - Wiley Online Library
Ectopic cardiac fatty images are not rarely detected incidentally by computed tomography and cardiac magnetic resonance, or by exams focused on the heart as in general thoracic …
The objective of the study was to perform a retrospective pilot study to evaluate the potential of myocardial T1 in assessment of Duchenne muscular dystrophy (DMD) cardiomyopathy …
ICC Barbin, JA Pereira, M Bersan Rovere… - Journal of …, 2016 - Wiley Online Library
We examined the effects of exercise on diaphragm degeneration and cardiomyopathy in dystrophin‐deficient mdx mice. Mdx mice (11 months of age) were exercised (swimming) for …
SM Schneider, V Sridhar, AK Bettis… - Molecular imaging and …, 2018 - Springer
Abstract Purpose Metabolic dysfunction in Duchenne muscular dystrophy (DMD) is characterized by reduced glycolytic and oxidative enzymes, decreased and abnormal …