Hyperammonemia can be caused by various acquired or inherited disorders such as urea
cycle defects. The brain is much more susceptible to the deleterious effects of ammonium in …

Congenital portosystemic shunts are present in one in 30,000 children. Among the
associated risks of severe complications are neonatal cholestasis, benign and malignant …

Congenital portosystemic venous shunts are rare developmental anomalies resulting in
diversion of portal flow to the systemic circulation and have been divided into extra-and …

Objective: To propose an anatomical classification of congenital portosystemic shunts
(CPSs) correlating with conservative surgery. Background: CPSs entail a risk of life …

A deficiency of each of the three enzymes important in galactose metabolism, galactose-1-
phosphate uridyltransferase (GALT), galactokinase (GALK) and UDP-galactose 4 …

Background: Congenital portosystemic shunts (CPSS) are rare vascular anomalies resulting
in communications between the portal venous system and the systemic venous circulation …

Congenital portosystemic shunts are developmental abnormalities of the portal venous
system resulting in the diversion of portal blood away from the liver to the systemic venous …

BACKGROUND Abernethy syndrome is a congenital vascular anomaly in which the portal
blood completely or partially bypasses the liver through a congenital portosystemic shunt …

Purpose To assess the utility of preoperative venography in evaluating and managing
patients with congenital portosystemic shunts (CPSSs). Materials and Methods A …

Objective: The aim of this single-center retrospective study was to analyze the clinical
characteristics, treatment options, and course of neonatal-onset congenital portosystemic …