Abstract Neurofibromatosis type 1 (NF1), neurofibromatosis type 2 (NF2), and
schwannomatosis (SWN) are three clinically distinct tumor predisposition syndromes with a …

One of the most common malignancies affecting adults with the neurofibromatosis type 1
(NF1) cancer predisposition syndrome is the malignant peripheral nerve sheath tumor …

PREAMBLE The Society of Nuclear Medicine and Molecular Imaging (SNMMI) is an
international scientific and professional organization founded in 1954 to promote the …

Malignant peripheral nerve sheath tumors (MPNSTs) are aggressive soft tissue sarcomas
(STS) with nerve sheath differentiation and a tendency to metastasize. Although occurring at …

Peripheral nerve sheath tumors are commonly encountered and frequently pose challenges
to the pathologist and the clinician. This review discusses the wide range of entities with an …

Objective To determine the utility of quantitative metrics obtained from fMRI using diffusion-
weighted imaging (DWI)/apparent diffusion coefficient (ADC) mapping compared with …

Abstract Neurofibromatosis type 1 (NF1) is an autosomal dominant hereditary tumor
syndrome, with a wide clinicopathologic spectrum. It is defined by characteristic central …

Background Plexiform neurofibromas (PN) are congenital tumors that affect up to 50% of
individuals with neurofibromatosis type 1. Despite their benign nature, they can grow rapidly …

Purpose Detecting malignant peripheral nerve sheath tumors (MPNSTs) remains difficult.
18F-FDG PET-CT has been shown helpful, but ideal threshold values of semi-quantitative …

Accurate staging and response assessment is vital in the management of childhood
malignancies. Fluorine-18 fluorodeoxyglucose positron emission tomography/CT (FDG PET …