[HTML][HTML] Update on the pathology of pediatric liver tumors: A pictorial review

P Bhagat, M Vij, LP Raju, G Gowrishankar, J Menon… - Diagnostics, 2023 - mdpi.com
Liver tumors in children are uncommon and show remarkable morphologic heterogeneity.
Pediatric tumors may arise from either the epithelial or mesenchymal component of the liver …

[HTML][HTML] Current scenarios of pediatric transplants of kidney, liver, heart, and lung in India: systematic review and meta-analysis

VB Kute, M Rela, S Gulati, AK Bhalla, G Abraham… - Exp Clin …, 2022 - ectrx.org
Objectives: There is no systematic review and meta-analysis for pediatric solid-organ
transplants in India. The objective of the study was to collect high-evidence data in this …

[HTML][HTML] Hypertyrosinemia

M Adnan, S Puranik - 2022 - europepmc.org
Objectives: Describe different causes of hypertyrosinemia. Explain etiopathogenesis and
modes of presentation of the different types of hypertyrosinemia. Outline management …

Pathologic and Immunophenotypic Characterization of Syncytial Giant Cell Variant of Pediatric Hepatocellular Carcinoma. A Distinct Subtype

M Vij, J Menon, K Subbiah, LP Raju… - Fetal and Pediatric …, 2023 - Taylor & Francis
Introduction Hepatocellular carcinoma (HCC) in pediatrics has a uniformly poor prognosis.
Complete surgical resection or liver transplantation remain the only curative options. In …

[PDF][PDF] Molecular docking and QSAR studies for modeling the inhibitory activity of pyrazole-benzimidazolone Hybrids as Novel Inhibitors of Human 4 …

NN Mrabti, HN Mrabti, Z Khalil… - … Res. Appl. Chem, 2022 - researchgate.net
Pyrazole-benzimidazolone is a novel inhibitor of human 4-Hydroxyphenylpyruvate
dioxygenase of the HPPD receptor. To analyze this inhibitory activity, a QSAR study was …

[PDF][PDF] E. coli´ s fight against TYROnny: Designing a bacterial strain to tackle tyrosinemia type 1

J Lücke, S Huber - Journal of Hepatology, 2023 - researchgate.net
EcN-HT led to a 100% survival of Fah-deficient mice, while all mice treated with EcN
succumbed to their disease after 50 days. Furthermore, SA, AST, ALT, and creatinine levels …

Liver transplantation for tyrosinemia type 1 in the developing world: is it really the best we can offer?

R Bolia, A Srivastava - Indian Journal of Pediatrics, 2022 - Springer
In this issue of the Journal, Menon et al. have reported their experience with liver
transplantation (LT) in 9 children with tyrosinemia type 1 (TT1). The authors concluded that …

Decoding hepatorenal tyrosinemia type 1: Unraveling the impact of early detection, NTBC, and the role of liver transplantation

M Kehar, M Sen Sarma, J Seetharaman… - Canadian Liver …, 2024 - canlivj.utpjournals.press
Abstract Hepatorenal tyrosinemia type 1 (HT-1) is a rare autosomal recessive disease that
results from a deficiency of fumaryl acetoacetate hydrolase (FAH), a critical enzyme in the …

[图书][B] Studies on the Acute Porphyrias–With Special Reference to Women's Health

D Vassiliou - 2023 - search.proquest.com
The acute porphyrias are a group of rare inherited disorders of the metabolism of heme.
Three acute porphyrias comprise most of the cases: acute intermittent porphyria (AIP) …

Liver transplantation for tyrosinemia type 1 in the developing world: is it really the best we can offer?: correspondence

J Menon, N Shanmugam, M Rela - Indian Journal of Pediatrics, 2022 - Springer
To the Editor: We read with interest the editorial comment [1] on our publication “Liver
Transplantation: A Safe and Definitive Alternative to Lifelong Nitisinone for Tyrosinemia …