Several familial syndromes are associated with an increased incidence of nervous system
tumors. Recognition of these syndromes is critical to provide optimal clinical care and …

Vascular lesions of the orbit may be classified on the basis of their natural history, growth
pattern, and histologic composition as capillary hemangiomas, venous vascular …

Object. Von Hippel—Lindau (VHL) disease is an autosomal-dominant disorder frequently
associated with hemangioblastomas of the spinal cord. Because of the slow progression …

Object In the course of their lives most patients with von Hippel–Lindau (VHL) disease
require treatment for several symptom-producing hemangioblastomas of the cerebellum …

Object Despite the frequency of cerebellar hemangioblastomas in von Hippel–Lindau (VHL)
disease, their optimum contemporary management has not been defined, and is made …

von Hippel–Lindau (VHL) disease is a rare, autosomal dominantly inherited multisystem
disorder characterized by development of a variety of benign and malignant tumors. The …

The present third edition of the clinical guideline is the result of a thorough revision. The
diagnostic criteria have been changed: There is no longer a distinction between major and …

Object. Hemangioblastomas of the brainstem constitute 5 to 10% of central nervous system
(CNS) tumors in patients with von Hippel—Lindau (VHL) disease. At present, optimal …

Poulsen MLM, Budtz‐Jørgensen E, Bisgaard ML. Surveillance in von Hippel‐Lindau
disease (vHL). von Hippel‐Lindau disease (vHL) is a hereditary multisystem cancer …

The hypothalamus is susceptible to involvement by a variety of processes, including
developmental abnormalities, primary tumors of the central nervous system (CNS), vascular …