Perivascular epithelioid cell tumors are mesenchymal neoplasms defined by the presence of
histologically and immunohistochemically distinctive perivascular epithelioid cells. The …

The uterus and retroperitoneum have emerged as the most frequently reported anatomic
sites of origin of perivascular epithelioid cell tumors (PEComas), a poorly defined neoplasm …

An increasing number of TFE3 rearrangement–associated tumors, such as TFE3
rearrangement–associated perivascular epithelioid cell tumors (PEComas), melanotic Xp11 …

We describe 2 cases of malignant melanotic epithelioid renal neoplasms bearing TFE3
gene fusions. Both neoplasms occurred in children (an 11-y-old boy and a 12-y-old girl), and …

Simple Summary In this article, we review the clinical features of advanced PEComas and
show the diversity of reported data among authors, emphasizing the heterogeneity of …

Perivascular epithelioid tumor (PEComa), a recently defined tumor, is a very rare disease
affecting various organs, most often the uterus. This tumor displays a variety of histologic …

Background Perivascular epithelioid cell tumors (PEComas) are rare mesenchymal
neoplasms of uncertain malignant potential, which have in common the co-expression of …

PEComa of the gastrointestinal tract, composed of perivascular epithelioid cells with
myomelanocytic differentiation, is rare with previous literature limited to 16 case reports …

The connection between angiomyolipoma (AML) of the kidney, clear cell sugar tumor
(CCST) of the lung, and pulmonary lymphangioleiomyoma (LAM), was progressively …

Perivascular epithelioid cell tumor (PEComa) is a rare tumor which arises from
mesenchymal tissues. It is predominant in the uterus, but very rare in the liver. To the best of …