Systemic amyloidosis from A (AA) to T (ATTR): a review

E Muchtar, A Dispenzieri, H Magen… - Journal of internal …, 2021 - Wiley Online Library
Systemic amyloidosis is a rare protein misfolding and deposition disorder leading to
progressive organ failure. There are over 15 types of systemic amyloidosis, each caused by …

Comprehensive review of AL amyloidosis: some practical recommendations

R Al Hamed, AH Bazarbachi, A Bazarbachi… - Blood Cancer …, 2021 - nature.com
Amyloid light chain (AL) amyloidosis is among the more common and more severe of the
amyloidoses usually involving the slow proliferation of a bone-marrow-residing plasma cell …

Diagnosis and treatment of cardiac amyloidosis: a position statement of the ESC Working Group on Myocardial and Pericardial Diseases

P Garcia-Pavia, C Rapezzi, Y Adler, M Arad… - European heart …, 2021 - academic.oup.com
Cardiac amyloidosis is a serious and progressive infiltrative disease that is caused by the
deposition of amyloid fibrils at the cardiac level. It can be due to rare genetic variants in the …

Diagnosis and treatment of cardiac amyloidosis. A position statement of the European Society of Cardiology W orking G roup on M yocardial and P ericardial D …

P Garcia‐Pavia, C Rapezzi, Y Adler… - European journal of …, 2021 - Wiley Online Library
Cardiac amyloidosis is a serious and progressive infiltrative disease that is caused by the
deposition of amyloid fibrils at the cardiac level. It can be due to rare genetic variants in the …

Marked progress in AL amyloidosis survival: a 40-year longitudinal natural history study

A Staron, L Zheng, G Doros, LH Connors… - Blood cancer …, 2021 - nature.com
The recent decades have ushered in considerable advancements in the diagnosis and
treatment of systemic light chain (AL) amyloidosis. As disease outcomes improve, AL …

Prognosis and staging of AL amyloidosis

T Dittrich, C Kimmich, U Hegenbart… - Acta haematologica, 2020 - karger.com
The treatment options for systemic light chain amyloidosis (AL) are currently widening in an
unprecedented way, brought about by an expanding arsenal of anti-myeloma therapy as …

[HTML][HTML] Light chain amyloidosis: epidemiology, staging, and prognostication

KR Baker - Methodist DeBakey Cardiovascular Journal, 2022 - ncbi.nlm.nih.gov
Amyloidosis is a disorder of protein misfolding and metabolism in which insoluble fibrils are
deposited in various tissues, causing organ dysfunction and eventually death. Out of the 60 …

Ventricular arrhythmias in cardiac amyloidosis: a review of current literature

S Khanna, P Lo, K Cho… - Clinical Medicine Insights …, 2020 - journals.sagepub.com
Cardiac Amyloidosis is an infiltrative cardiomyopathy which occurs secondary to deposition
of mis-folded protein in the myocardium, with the two most common subtypes being AL …

New developments in diagnosis, risk assessment and management in systemic amyloidosis

I Vaxman, A Dispenzieri, E Muchtar, M Gertz - Blood reviews, 2020 - Elsevier
Amyloidosis is a group of disorders characterized by a misfolded protein that deposits in
organs and compromise their function. Clinician should have a high index of suspicion …

[HTML][HTML] Electrocardiographic Patterns and Arrhythmias in Cardiac Amyloidosis: From Diagnosis to Therapeutic Management—A Narrative Review

L Teresi, G Trimarchi, P Liotta… - Journal of Clinical …, 2024 - pmc.ncbi.nlm.nih.gov
Electrophysiological aspects of cardiac amyloidosis (CA) are still poorly explored compared
to other aspects of the disease. However, electrocardiogram (ECG) abnormalities play an …