Molecular basis of rare congenital bleeding disorders
A Dorgalaleh, M Bahraini, M Shams, F Parhizkari… - Blood Reviews, 2023 - Elsevier
Rare bleeding disorders (RBDs), including factor (F) I, FII, FV, FVII, combined FV and FVIII
(CF5F8), FXI, FXIII and vitamin-K dependent coagulation factors (VKCF) deficiencies, are a …
(CF5F8), FXI, FXIII and vitamin-K dependent coagulation factors (VKCF) deficiencies, are a …
Inhibitors of blood coagulation factor XIII
T Schmitz, CA Bäuml, D Imhof - Analytical biochemistry, 2020 - Elsevier
The blood coagulation factor XIII (FXIII) plays an essential role in the stabilization of fibrin
clots. This factor, belonging to the class of transglutaminases, catalyzes the final step of …
clots. This factor, belonging to the class of transglutaminases, catalyzes the final step of …
Factor XIII Deficiency: Laboratory, Molecular, and Clinical Aspects
A Dorgalaleh, S Jozdani… - Seminars in Thrombosis …, 2024 - thieme-connect.com
Factor XIII-A (FXIII-A) deficiency is an ultra-rare bleeding disorder characterized by high
rates of morbidity and mortality, primarily resulting from intracranial hemorrhage, umbilical …
rates of morbidity and mortality, primarily resulting from intracranial hemorrhage, umbilical …
Genetic landscape in coagulation factor XIII associated defects–Advances in coagulation and beyond
H Javed, S Singh, SUR Urs, J Oldenburg, A Biswas - Blood Reviews, 2023 - Elsevier
Coagulation factor XIII (FXIII) acts as a fine fulcrum in blood plasma that maintains the
balance between bleeding and thrombosis by covalently crosslinking the pre-formed fibrin …
balance between bleeding and thrombosis by covalently crosslinking the pre-formed fibrin …
Identification of potential novel interacting partners for coagulation factor XIII B (FXIII-B) subunit, a protein associated with a rare bleeding disorder
S Singh, MS Akhter, J Dodt, P Volkers, A Reuter… - International journal of …, 2019 - mdpi.com
Coagulation factor XIII (FXIII) is a plasma-circulating heterotetrameric pro-transglutaminase
complex that is composed of two catalytic FXIII-A and two protective/regulatory FXIII-B …
complex that is composed of two catalytic FXIII-A and two protective/regulatory FXIII-B …
Distinct 3-disulfide-bonded isomers of tridegin differentially inhibit coagulation factor XIIIa: The influence of structural stability on bioactivity
CA Baeuml, AAP George, T Schmitz… - European Journal of …, 2020 - Elsevier
Tridegin is a 66mer cysteine-rich coagulation factor XIIIa (FXIIIa) inhibitor from the giant
amazon leech Haementeria ghilianii of yet unknown disulfide connectivity. This study covers …
amazon leech Haementeria ghilianii of yet unknown disulfide connectivity. This study covers …
Hypochlorite-Induced Disturbance in the Secondary Structure of the Coagulation Factor XIII
AN Shchegolikhin, AD Vasilyeva, LV Yurina… - Russian Journal of …, 2021 - Springer
Coagulation factor XIII (FXII), which is converted into the active form of FXIIIa under the
combined action of thrombin and calcium ions, plays an important role in the processes of …
combined action of thrombin and calcium ions, plays an important role in the processes of …
[引用][C] 4.3 Chapter III-Distinct 3-disulfide-bonded isomers of tridegin differentially inhibit coagulation factor XIIIa: The influence of structural stability on bioactivity
CA Bäuml, AAP George, T Schmitz, P Sommerfeld… - Influence of disulfide-bonds …, 2021