Background: Desmoplastic small round-cell tumor (DSCRT) in adults is an extremely rare
(age-adjusted incidence 0.3 per million) and aggressive sarcoma with limited data for …

Abstract Desmoplastic Small Round Cell Tumors (DSRCTs) are an entity of rare, aggressive
soft tissue sarcomas described by Gerald and Rosai in 1989. It predominantly affects male …

Desmoplastic small round cell tumor (DSRCT) is characterized by the EWSR1–WT1 t (11;
22)(p13: q12) translocation. Few additional putative drivers have been identified, and …

Desmoplastic small round cell tumor is a very rare and highly aggressive soft tissue
sarcoma, usually presenting with multiple intra-abdominal tumors in young males. Patients …

Abstract In the United States, more than 10 000 cancers occur annually in children aged 0–
14 years, and more than 5000 in adolescents aged 15–19. In the last 50 years, significant …

Desmoplastic small round cell tumor (DSRCT) is a rare malignant tumor with poor
prognosis, usually involving the peritoneum. There are currently no standardized treatment …

Aim: This single-centre study evaluated cytoreductive surgery (CRS) combined with
hyperthermic intraperitoneal chemotherapy (HIPEC) for patients with rare histologies and …

Background Desmoplastic small round cell tumor (DSRCT) is a rare, aggressive,
mesenchymal malignancy of a separate clinicopathological entity. It has a predilection for …

With an annual cumulative occurrence of approximately 15,000 in North America, all
childhood cancers are rare. Very rare cancers as defined by both the European Cooperative …

Аннотация Десмопластическая мелкокруглоклеточная опухоль (ДМКО)—очень редкая и
агрессивная злокачественная опухоль брюшной полости, впервые описанная в 1989 …