Update on the pathogenesis, clinical diagnosis, and treatment of Hirayama disease

H Wang, Y Tian, J Wu, S Luo, C Zheng, C Sun… - Frontiers in …, 2022 - frontiersin.org
Hirayama disease (HD) is characterized by the juvenile onset of unilateral or asymmetric
weakness and amyotrophy of the hand and ulnar forearm and is most common in males in …

Diagnosis and clinical management of amyotrophic lateral sclerosis and other motor neuron disorders

SA Goutman - CONTINUUM: Lifelong Learning in Neurology, 2017 - journals.lww.com
Abstract Purpose of Review: This article reviews the clinical features, diagnostic pathway,
therapies, and current understanding of the pathophysiology of amyotrophic lateral sclerosis …

Hirayama disease

YL Huang, CJ Chen - Neuroimaging Clinics, 2011 - neuroimaging.theclinics.com
Hirayama disease is a benign, self-limiting cervical myelopathy first brought to attention by
Hirayama 1 in 1959. During the past half century, researches have established this disease …

Multilevel spinal stabilization as a treatment for Hirayama disease: report of an experience with five cases

A Goel, A Dhar, A Shah - World Neurosurgery, 2017 - Elsevier
Objective To analyze the role of multisegmental spinal instability in the pathogenesis of
Hirayama disease. Material and Methods From June 2014 to January 2016, the authors …

Clinical and radiological profile of Hirayama disease: a flexion myelopathy due to tight cervical dural canal amenable to collar therapy

KM Hassan, H Sahni, A Jha - Annals of Indian Academy of …, 2012 - journals.lww.com
Background: Hirayama disease (HD) is benign focal amyotrophy of the distal upper limbs,
often misdiagnosed as motor neuron disease. Routine magnetic resonance imaging (MRI) is …

Hirayama disease: Nosological classification and neuroimaging clues for diagnosis

S Iacono, V Di Stefano, A Gagliardo… - Journal of …, 2022 - Wiley Online Library
Hirayama disease (HD) is a rare, benign, and nonprogressive motor neuron disease (MND)
affecting the upper limbs. It usually presents with weakness and amyotrophy in a single …

Forward shifting of posterior dural sac during flexion cervical magnetic resonance imaging in Hirayama disease: an initial study on normal subjects compared to …

V Lai, YC Wong, WL Poon, MK Yuen, YP Fu… - European journal of …, 2011 - Elsevier
OBJECTIVE: Forward shifting of the posterior cervical dural sac is the most important sign in
diagnosing Hirayama disease but can also be seen in normal subjects, causing potential …

Cervical spine MR imaging findings of patients with Hirayama disease in North America: a multisite study

VT Lehman, PH Luetmer… - American Journal …, 2013 - Am Soc Neuroradiology
BACKGROUND AND PURPOSE: Most studies of HD have been conducted in Asia,
particularly Japan. To characterize the MR imaging findings of North American patients with …

The importance of flexion MRI in Hirayama disease with special reference to laminodural space measurements

DK Boruah, A Prakash, BB Gogoi… - American Journal …, 2018 - Am Soc Neuroradiology
BACKGROUND AND PURPOSE: Hirayama disease is a benign focal amyotrophy of the
distal upper limbs involving C7, C8, and T1 segmental myotomes with sparing of the …

MRI findings in Hirayama disease

M Raval, R Kumari, AAD Dung… - Indian Journal of …, 2010 - thieme-connect.com
The objective of the study was to study the magnetic resonance imaging (MRI) features of
Hirayama disease on a 3 Tesla MRI scanner. Nine patients with clinically suspected …