Developments in managing CF continue to drive dramatic improvements in survival. As
newborn screening rolls-out across Europe, CF centres are increasingly caring for cohorts of …

Specialised CF care has led to a dramatic improvement in survival in CF: in the last four
decades, well above what was seen in the general population over the same period. With …

Background Malnutrition is both a frequent feature and a comorbidity of cystic fibrosis (CF),
with nutritional status strongly associated with pulmonary function and survival. Nutritional …

Cystic fibrosis (CF) is the most common autosomal recessive disease in the Caucasian
population. Cystic fibrosis-related liver disease (CFLD) is defined as the pathogenesis …

Each Association appointed at least one author to serve on the writing group. The Chair of
the writing group was appointed by the AASLD. Members of the writing group were not …

Cystic fibrosis (CF)‐associated liver disease (CFLD) is a hepatobiliary complication of CF.
Current diagnostic modalities rely on nonspecific assessments, whereas liver biopsy is the …

Peribiliary glands (PBG) are a source of stem/progenitor cells organized in a cellular
network encircling large bile ducts. Severe cholangiopathy with loss of luminal biliary …

Background Universal screening of newborn babies for cystic fibrosis was launched in
Germany on 1 September 2016. Here we present up-to-date information on the diagnosis …

Cystic fibrosis is a life-limiting, recessive disease caused by mutations in the cystic fibrosis
transmembrane conductance regulator (CFTR) gene. Increased survival outcomes and the …

Cystic fibrosis (CF) is a common lethal genetic disease in the North American population,
affecting 1: 2500 births. There are about 30,000 individuals in the United States with CF, and …