Interstitial lung diseases

M Wijsenbeek, A Suzuki, TM Maher - The Lancet, 2022 - thelancet.com
Over 200 interstitial lung diseases, from ultra rare to relatively common, are recognised.
Most interstitial lung diseases are characterised by inflammation or fibrosis within the …

Pulmonary fibrosis: from pathogenesis to clinical decision-making

T Koudstaal, M Funke-Chambour, M Kreuter… - Trends in molecular …, 2023 - cell.com
Pulmonary fibrosis (PF) encompasses a spectrum of chronic lung diseases that
progressively impact the interstitium, resulting in compromised gas exchange …

Outcome of hospitalization for COVID-19 in patients with interstitial lung disease. An international multicenter study

TM Drake, AB Docherty, EM Harrison… - American journal of …, 2020 - atsjournals.org
Rationale: The impact of coronavirus disease (COVID-19) on patients with interstitial lung
disease (ILD) has not been established. Objectives: To assess outcomes in patients with ILD …

Cyclophosphamide added to glucocorticoids in acute exacerbation of idiopathic pulmonary fibrosis (EXAFIP): a randomised, double-blind, placebo-controlled, phase …

JM Naccache, S Jouneau, M Didier, R Borie… - The Lancet …, 2022 - thelancet.com
Background The use of cyclophosphamide in patients with acute exacerbation of idiopathic
pulmonary fibrosis (IPF) is unknown. Our study was designed to evaluate the efficacy and …

Interstitial lung disease in connective tissue disease: a common lesion with heterogeneous mechanisms and treatment considerations

T Shao, X Shi, S Yang, W Zhang, X Li, J Shu… - Frontiers in …, 2021 - frontiersin.org
Connective tissue disease (CTD) related interstitial lung disease (CTD-ILD) is one of the
leading causes of morbidity and mortality of CTD. Clinically, CTD-ILD is highly heterogenous …

Acute exacerbation of interstitial lung disease associated with rheumatic disease

F Luppi, M Sebastiani, C Salvarani… - Nature Reviews …, 2022 - nature.com
Interstitial lung disease (ILD) is a cause of morbidity and mortality in patients with rheumatic
diseases, such as connective-tissue diseases, rheumatoid arthritis and systemic vasculitis …

Practical considerations for the diagnosis and treatment of fibrotic interstitial lung disease during the coronavirus disease 2019 pandemic

AW Wong, L Fidler, V Marcoux, KA Johannson… - Chest, 2020 - Elsevier
The coronavirus disease 2019 (COVID-19) pandemic, caused by severe acute respiratory
syndrome coronavirus 2, has affected virtually all aspects of patient care. Health-care …

Inhibition of lung microbiota-derived proapoptotic peptides ameliorates acute exacerbation of pulmonary fibrosis

CN D'Alessandro-Gabazza, T Yasuma… - Nature …, 2022 - nature.com
Idiopathic pulmonary fibrosis is an incurable disease of unknown etiology. Acute
exacerbation of idiopathic pulmonary fibrosis is associated with high mortality. Excessive …

Treatment of idiopathic pulmonary fibrosis and progressive pulmonary fibrosis: A position statement from the Thoracic Society of Australia and New Zealand 2023 …

JA Mackintosh, G Keir, LK Troy, AE Holland… - …, 2024 - Wiley Online Library
Idiopathic pulmonary fibrosis (IPF) is a progressive disease leading to significant morbidity
and mortality. In 2017 the Thoracic Society of Australia and New Zealand (TSANZ) and Lung …

Idiopathic pulmonary fibrosis

F León-Román, C Valenzuela… - Medicina Clínica (English …, 2022 - Elsevier
Idiopathic pulmonary fibrosis is defined as a chronic progressive fibrosing interstitial
pneumonia of unknown etiology. There are intrinsic and extrinsic risk factors that could favor …