The aim of a clinical classification of pulmonary hypertension (PH) is to group together
different manifestations of disease sharing similarities in pathophysiologic mechanisms …

Pulmonary arterial hypertension (PAH) is a chronic and progressive disease leading to right
heart failure and ultimately death if untreated. The first classification of PH was proposed in …

Pulmonary hypertension (PH) is a heterogeneous condition. To date, no registry data exists
reflecting the spectrum of disease across the five diagnostic groups encountered in a …

Background Data on survival and prognosis factors in incident cohorts are scarce in
systemic sclerosis (SStc). To describe survival, standardized mortality ratio (SMR), and …

Systemic sclerosis (SSc) is a chronic immune disorder of unknown origin, dominated by
excessive fibrosis responsible for cutaneous and pulmonary fibrosis, and by vascular …

Primary cardiac involvement, which develops as a direct consequence of systemic sclerosis
(SSc), may manifest as myocardial damage, fibrosis of the conduction system, pericardial …

Objectives: To measure the prevalence of, and factors associated with, left ventricular (LV)
dysfunction in systemic sclerosis (SSc). Methods: The EUSTAR database was first searched …

Objectives: To assess the prevalence and patterns of cardiac abnormalities as detected by
cardiac magnetic resonance imaging (MRI) in systemic sclerosis (SSc). Methods: Fifty-two …

Background: Primary cardiac affection is common and is a major cause of death in systemic
sclerosis (SSc), but there are knowledge gaps regarding the effect of cardiac dysfunction on …

Idiopathic pulmonary fibrosis (IPF) is a disabling disease of the lung parenchyma,
characterized by progressive accumulation of scar tissue and myofibroblast activation after …